Prune belly syndrome a rare case report

ABSTRACT

A case of a rare congenital anomaly of Prune Belly Syndrome (PBS) predominant in males is presented. 1 Incidence is 1 in 40;000 lives births. The complete syndrome is characterized by ; dilatation of the upper urinary tract; lateral deviation of the dilated ureters large bladder with urachal anomalies; vesicoureteral reflux; dilatation of the prostatic utricle; undescended testis and patchy agenesis of the anterior 2 abdominal wall. All the above features may not necessarily be present in one single case. The major anomaly is due to failure of proper development of both the urinary tract and anterior abdominal wall. Respiratory; cardiac; skeletal and anorectal malformations may be present as well