Sturge-weber diseases without facial nevus

We report a patient with Sturge-Weber Disease who presented with intractable seizures and intellectual deterioration. There were no facial or scalp lesions. Brain CT showed left parieto-occipital calcification. The patient was treated surgically and the histology confirmed the diagnosis of Sturge-Weber disease. The diagnosis and clinical management of this rare variant of Sturge-Weber disease without a facial naevus are discussed