ABSTRACT
Pigmented epithelioid melanocytoma (PEM) is a borderline melanocytic neoplasms or a low-grade melanoma which is rare. It affects all age groups. The prognosis is relatively good compared to conventional malignant melanoma. We presented here a case of 3 years old Saudi girl presented with an asymptomatic brown-black lesion on her left forearm. At clinical examination,the lesion had a diameter of 0.6 cm, appeared round, exophytic, and intensely pigmented with well-defined edges and bluish reflections. All features strongly suggested nodular melanoma and the lesion was excised and histopathology showed asymmetrical growth of heavily pigmented atypical epithelioid and spindle cells. A pigmented epithelioid melanocytoma, so-called animal-type melanoma, was diagnosed. The depth of invasion was classified as Clark level IV, with maximum thickness of 3 mm.