Nephron-Sparing Surgery for Giant Angiomyolipoma of the Kidney.

Renal angiomyolipomas are rare benign tumors known to occur sporadically and in association with genetic syndromes, tuberous sclerosis and lymphangioliomyomatosis. Surgical removal or radiographic embolisation of angiomyolipomas larger than 4 cm is usually indicated because of an increased risk of spontaneous hemorrhage. We describe successful nephron-sparing surgery for a giant angiomyolipoma and discuss relevant management issues in a patient with angiomyolipoma.