[Primary intestinal lymphangiectasia in a patient with polyglandular autoimmune disease]

Primary intestinal lymphangiectasia is a rare disorder that is not commonly associated with autoimmune phenomena. We report a case of a 29-year-old man with primary lymphangiectasia who additionally had vitiligo, autoimmune hypothyroidism, hypogonadism, and pernicious anemia. We speculate that autoimmunity may play a role in the pathogenesis of primary intestinal lymphangiectasia