Local fibrocartilaginous dysplasia: an unusual cause of tibial vara

We report on one case with tibia vara caused by focal fibrocartilaginous dysplasia [FFD] of the medial aspect of the proximal tibia A Kuwaiti boy 4 1/2 years of age had developed a progressive deformity of the right proximal tibia between the age of 2 and 4 which on presentation had reached 35 degrees of varus deformity Because conservative management is recommended in the literature, and also because some reduction in the deformity was observed after the age of 4, surgery was postponed Indeed, the excellent response observed with conservative management makes recognition of this disease entity Important The condition is exceedingly rare with only 25 cases having been described in the world literature up to the present