Cleidocranial dysplasia- a case report and literature review

Cleidocranial dyspalsia is a rare congenital skeletal disorder, associated with hypoplasia or aplasia of clavicles, delayed closure of cranial sutures and fontanels, frontoparietal bossing, delayed exfoliation of primary dentition, delayed or failure of eruption of permanent teeth, and presence of multiple supernumerary teeth. The disorder is caused by mutation in the CBFA1 gene, on the short arm of chromosome 6p21. Estimated prevalence ofcleidocranial dysplasia is one per million, without gender or ethnic predilection. A multidisciplinary approach is often required for dental management of multiple supernumerary teeth. We report clinical and radiographic presentation and surgical management of multiple supernumerary teeth in an 11-year-old child with cleidocranial dysplasia.

Management of obstructive sleep apnea and facial asymmetry by distraction osteogenesis of mandible

Micrognathia and obstructive sleep apnea syndrome [OSAS] are problems subsequent to temporomandibular joint ankylosis [TMJa] in growing patients. For patients with micrognathia and OSAS secondary to TMJa, it is important to restore proper mandibular form and posterior facial height, achieve occlusal stability and satisfactory mouth opening. We report a 2-year follow-up of a patient with Micronesia and OSAS secondary to unilateral TMJ ankylosis of the right side. The patient had an operation of TMJa before she reported to us but mouth opening was limited. The treatment involved vertical ramus osteotomy, coronoidectomy and external distraction osteogenesis of her mandible. After the treatment of micrognathia oropharyngeal airway space was increased, patient was followed up for 2 years and the results remain uneventful