ABSTRACT
A homocystinuric child presented with a secondary pupillary block glaucoma due to anteriorly subluxated lens. After removal of the subluxated lens, a suture supported posterior chamber IOL was implanted. Postoperative complication of cerebral venous thrombosis following general anaesthesia was managed with high doses of pyridoxine special diet and drugs.
Subject(s)
Anesthesia, General/adverse effects , Child , Glaucoma/complications , Homocystinuria/complications , Humans , Intracranial Embolism and Thrombosis/etiology , Lens Implantation, Intraocular/methods , Lens Subluxation/complications , Suture TechniquesABSTRACT
A full term female baby at birth showed the features of Fraser's syndrome viz. upper lid coloboma, cryptophthalmos, abnormal groove over temporal region, dysmorphic facies, hypospadias and bilateral syndactyly. On ultrasound examination of the abdomen and left orbit, maldeveloped kidney and eyeball were found. Other siblings were not affected. The child died at the age of 3 months.
Subject(s)
Abnormalities, Multiple/diagnostic imaging , Coloboma/diagnostic imaging , Eyelids/abnormalities , Facial Bones/abnormalities , Female , Humans , Infant, Newborn , Kidney/abnormalities , Syndactyly/diagnostic imaging , SyndromeABSTRACT
Melanocytoma of the optic disc is a benign lesion. We report here a patient with melanocytoma who presented with gradual diminution of vision. On examination the left eye fundus showed a mass uniformly dark black in colour, on the optic disc occupying the superotemporal quadrant. The mass completely obscured the fluorescence on fluorescein angiography and was thus differentiated from malignant melanoma.