Friedrich disease within the child [report of 7 cases]

Through the observation of seven cases we reported the epidemiological, clinical, paraclinical, evolutionary and therapeutical aspects of this disease. Epidemiologically, the sex ratio is of 0,75. The medium age is of six years and two months. Factors in favor of a hereditary origin are the consanguinity found in 28,6% of cases and the presence of a similar case in the family observed in 42,3%. Clinically, the quasi constantly neurolgical signs are ataxia [100%], dysarthria [71, 4%], areflexia of endon reflex in both lowner limbs [57,14], deep sensation troubles are less frequent [28,6%]. Vestibular affection with form of horizontal nystagmus is found in 14,3% of cases. The dysmorphic syndrome is in the form of claw feet found in [57,14%] and of dorsal scoliosis in [14,3%]. Cardiac affection in the form of cardiopathy is noted in two magnetic resonance imagery in one patient. The electromyography is disturbed in 28.6% of cases. The genetic study done to two cases [28,6%]. Paraclinically, we found cerebellar atrophy in 57,14% which was confirmed by cases showed an expansion of the triplet GAA at the level of the chromosome nine. Improvement under symptomatic treatment based on muscular and functional physiotherapy was progressively slow for all our patients

Traitement chirurgical du cancer du col uterin [a prepos de 113 CAS]

We report in this study 113 cases of the cancer of uterine neck operated in obstetric gynecology [professor OSTOWAR] at the Souiss maternity of Rabat over a period from January 1st, 1970 to December 31st, 1990. 88 cases [77,88%] of our patients are multiparas.Average age is 41 with extremes of 20 and 70 years. [57,29%] are in a period of genital activity.30 cases [26,55%] are in a period of menaupose. The most frequent recealing sign is metrorrhagia, it is observed in 102 cases [90,27%]. The lack of precocions detection, of prophylaxy and hygiene make that the majority have come to consult at a late stage. Thus, almost half of them [49,56%] have come at stage IIB Budding and ulcero-budding forms are the most frequent 100 cases [88,50%] underwent surgical treatment of EIGS type. The other patients, 7 cases [6,19%] underwent a Weir theim and 6 cases [5,30%] did a hysterectomy. Prognosis is good in the majority of the cases, the number of cure is 93 cases [82,30%]. Yet, post-operation complications are especially ureteral 10 cases [8,85%]. Recurs are not rare: -12 cases of local recur-3 cases of for metastases