1.
Rev. méd. Panamá
; 18(3): 196-204, Sept. 1993.
Article
in Spanish
| LILACS
| ID: lil-410003
ABSTRACT
The authors present the clinical history of a patient with Marfan's syndrome (MS) and aortic insufficiency, who expired at 22 years of age, in order to illustrate the clinical evolution and review the management of this problem. It is known that patients with MS and heart failure due to dilatation of the aortic annulus have an early mortality of almost 100%. The authors conclude that echocardiographic follow up of these patients is vital in their medical and surgical management and that the use of beta blockers is the best medical therapy, and that prophylactic surgery with composite graft (aortic valve and ascending aorta) gives the best survival rate
Subject(s)
Humans , Male , Adult , Cardiovascular Diseases/diagnosis , Marfan Syndrome/diagnosis , Cardiovascular Diseases/etiology , Cardiovascular Diseases/pathology , Echocardiography , Electrocardiography , Aortic Valve Insufficiency/diagnosis , Aortic Valve Insufficiency/etiology , Aortic Valve Insufficiency/pathology , Marfan Syndrome/complications , Marfan Syndrome/pathology , Aortic Valve/pathology , Aortic Valve
2.
Bol. Asoc. Méd. P. R
; 74(4): 134-7, 1982.
Article
in English
| LILACS
| ID: lil-10458