ABSTRACT
Failure in the development of diaphragm leaves a posterolateral defect known as bochdalek hernia. This anomaly is observed on the left side in 80-90 percent of the cases. Incomplete development of the posterior diaphragm causes the abdominal viscera to move to the chest cavity, causing the lung to become hypoplastic at the affected side. Ectopic kidneys are mainly located within the pelvic. However rare cases of thoracic kidney have also been reported. The patient was a 2-months-old infant admitted to the pediatric ward in Kermanshah Imam Reza hospital. Chest x-ray and chest sonography revealed a right-sided diaphragmatic hernia with ectopic kidney within the right thorax. The patient underwent a surgery. It was a success and the patient was released from the hospital. Although thoracic kidney is a rare condition specifically when it is with diaphragmatic hernia, it could be diagnosed with before and after surgery investigations. This condition can be fixed with necessary manoeuvers and mobilization of vascular pediculus when the defect of diaphragm is removed