Bilateral Microcornea with Cornea Plana in a Family

Microcornea is a condition characterized by a small cornea in an otherwise normal eye and can be defined when corneal diameter is less than 11.00mm. Microcornea may occur as an isolated abnormality or accompany other anterior segment anomalies like aniridia and anterior chamber cleavage abnormalities. Microcornea is part of nanophthalmos, a condition in which a reduction in global dimensions is the only structural abnormality, as well as microphthalmos, a term generally, used to signify a small, abnormal globe. Microcornea is a rare anomaly and its etiology is probably a primary aberration of the growth of the ectoderm of the optic cup. Both autosomal dominant and autosomal recessive patterns of inheritance occur, but it may appear sporadically. Cornea plana is usually seen in association with microcornea wherein the corneal curvature is less than normal. It is often associated with diffuse opacities of the cornea stroma. Cornea plana might be caused by a deep developmental arrest in the fourth month, at which time the cornea begins to increase its curvature relative to the sclera. The authors experienced a case of bilateral microcornea with cornea plana in a family which seemed to transmit as the dominant trait.

Bilateral Microcornea with Cornea Plana in a Family

Microcornea is a condition characterized by a small cornea in an otherwise normal eye and can be defined when corneal diameter is less than 11.00mm. Microcornea may occur as an isolated abnormality or accompany other anterior segment anomalies like aniridia and anterior chamber cleavage abnormalities. Microcornea is part of nanophthalmos, a condition in which a reduction in global dimensions is the only structural abnormality, as well as microphthalmos, a term generally, used to signify a small, abnormal globe. Microcornea is a rare anomaly and its etiology is probably a primary aberration of the growth of the ectoderm of the optic cup. Both autosomal dominant and autosomal recessive patterns of inheritance occur, but it may appear sporadically. Cornea plana is usually seen in association with microcornea wherein the corneal curvature is less than normal. It is often associated with diffuse opacities of the cornea stroma. Cornea plana might be caused by a deep developmental arrest in the fourth month, at which time the cornea begins to increase its curvature relative to the sclera. The authors experienced a case of bilateral microcornea with cornea plana in a family which seemed to transmit as the dominant trait.

Surgical Correction of Convergent Strabismus Fixus

Convergent strabismus fixus is a rare condition in which one or both eyes are anchored in a position of extreme adduction. The involved eye is fixed in this position and cannot be moved, and the forced duction test will confirm the immobility of the eye. This condition generally is thought to be congenital and caused by fibrosis and loss of elasticity of the medial rectus muscle. However Villaseca postulated that fibrosis of the medial rectus muscle is the consequence of contracture following a lateral rectus paralysis rather than a primary anomaly. The authors experienced two cases of monocular convergent strabismus fixus of left eye in a 51 year old female patient and a 63 year old male patient. In the latter case, we performed complete disinsertion of medial rectus muscle combined with recession of conjunctiva and Tenon's capsule and temporary fixation of the globes with traction sutures in a position of abduction on left eye. The result of that surgery, however, was not satisfactory. So we performed 11mm resection of lateral rectus muscle of left eye about 8 weeks after the first surgery and followed up for months in satisfactory result.