ABSTRACT
Granulocytic sarcoma, a rare extramedullary solid tumor arising from early myeloid precursors, is capable of invading the meninges or the rain parenchyma. The tumor may occur during or after the onset of systemic myelogenous leukemia. On rare occasions, the tumor may evolve before the onset of systemic myelogenous leukemia. Children are affected more often than adults, but sex is not related. Although no definite target area of the brain can be demonstrated, there may be some predilection of the tumor for the posterior fossa. The authors report a case of 4-year-old-boy with granulocytic sarcoma occurring in the posterior fossa presenting with gait disturbance and torticollis. The patient was treated by surgical removal of the tumor, there by avoiding the potentially lethal complication of a posterior fassa mass. This rare case is reported together a review of the literature.