A Case of Systemic Sclerosis in a Child / 소아과

Systemic sclerosis is a connective tissue disease involving primarily the skin and subcutaneous tissue but may involve other organ systems such as the lungs, gastrointestinal tract, and heart. Systemic sclerosis is a rare childhood disease. The age of onset for patients with systemic sclerosis has its peak between 30 and 50 years of age. Only 1 to 2% of all patients with systemic sclerosis have disease onset before the age of 10 years of age. We report a case of systemic sclerosis in a 7-year-old female who showed Raynaud's phenomenon as an initial manifestation.

Analysis and Evaluation of the Reliability of Medical Information on Food Allergies on the Internet / 소아과

PURPOSE: The information in the internet is increasing and the number of people using the Internet to obtain medical information is increasing rapidly too. But, compared to the amount of information, the quality of information is extremely variable. To assess the accuracy of medical information on the Internet, the quality of information about food allergies available on the internet examined. METHODS: Online searches using the phrase "food allergy" were conducted on five major Internet search engines. The first 50 web pages generated by each engine were examined. Making an exception of the web pages which were inaccessible, irrelevant, and duplicated, sixty out of two hundred and fifty web pages were evaluated. Information scores were developed from 1(no statement) to 4 (sufficient) and designed to assess how well the web pages mentioned the summary, symptom, diagnosis, treatment, and education of the patients, and emergent management. RESULTS: When classified by ownership, there were six(10%) oriental clinics, twelve(20%) hospitals, twenty one(35%) profit-making institutions, fourteen(23%) non-profit institutions and seven others (12%). The mean information score(IS) was 10.7. Summary got the highest IS(2.25) and the education for patients and supporters got the lowest IS(1.33). Medical institutions such as hospital and clinic got 12.33 and non-medical institutions got 10.25. But there were no statistically significant differences between these two institutions(P=0.107). CONCLUSION: Overall, the quality of information on food allergy through the Internet was poor. The main reasons are unlimited listings of related information on the Internet and an absence of a reviewing process of the information. Therefore, people should not entirely rely on the Internet for medical information and medical-related institutions such as hospitals, schools, clinics and relevant academic associations should develop an Internet system to improve the quality of information.

A Case of the Diarrhea-associated Hemolytic Uremic Syndrome Developing Simultaneously with an Acute Appendicitis

Diarrhea-associated hemolytic uremic syndrome is rarely accompanied by complications requiring surgical intervention. We report a case of the diarrhea-associated hemolytic uremic sydrome which developed simultaneously with an acute appendicitis.

Characteristics of Children Whose First Seizure Attack Presented as Status Epilepticus / 대한소아신경학회지

PURPOSE: Status epilepticus(SE) is a pediatric and neurologic emergency associated with significant morbidity and mortality. Prompt recognition and management are needed for successful outcomes. We evaluated, clinical manifestations, treatment and prognosis of the patients whose first seizure attacks were presented as SE. METHODS: According to the department of pediatrics and the emergency room in Inha University Medical Center, there were a total of 25 children between 1 month and 5 years old who were diagnosed as status epilepticus from July 1996 to June 2002. Also, their medical records were reviewed and analyzed interms of age distribution, accompaning diseases, the types and duration of convulsion, medications, EEG and MRI findings and prognosis. RESULTS: Twenty-five cases were studied. The mean age at the time of the diagnosis was 20+/-1.6 months and 80% of the patients were less than 3 years old. The most common type of the status epilepticus was generalized tonic clonic seizure comprising 15 cases(60%). 64% of the patients were symptomatic:fever(40%), CNS infection(20%), ischemic injury(4%) while 36% were idiopathic. Seizure attacks were terminated within an hour in seventeen patients(68%) and they controlled by one antiepileptic drug in thirteen patients(52%). Of the 20 EEGs, abnormal findings were shown in 13 cases(65%); namely, electrical seizure(30%), abnormal background(30%), and focal epileptiform discharge(5%). Of the 19 brain MRIs, abnormal findings were shown in 9 cases(47%). CONCLUSION: The children whose first seizure attack were presented as SE were less than 3 years old. The prognosis is good in that most of the seizure attacks were terminated within an hour and controlled by one epileptic drug. However those seizure attacks with longer duration, multiple antiepileptic druge and underlying causeare had poor prognosis.