ABSTRACT
PURPOSE: Blue rubber bleb syndrome (BRBNS) is a rare disorder characterized by multiple, distinctive cavernous hemangiomas of the skin, and gastrointestinal tract. We investigated the surgical treatment and clinical findings for multiple hemangiomas in the orbit of a patient who had BRBNS on the skin and liver. METHODS: A 33-year-old white woman visited our clinic with the chief complaint of continuous exophthalmos of one year duration. She did not complain of ocular pain or decreased visual acuity. Nine years previously, her medical history showed the removal of a mass from her left arm, the result of histopathologic examination was multiple hemangiomas. Check-up for gastrointestinal lesions by colonoscopy was negative and all hematological parameters were normal. The orbital mass was surgically removed. Histopathological finding showed it to be the same as hemangioma. RESULTS: Multiple bluish nodules on the skin, visceral hemangioma, multiple hemangiomas in orbit led to the diagnosis of BRBNS. CONCLUSIONS: Multiple hemangiomas in orbit should be suspected as BRBNS, and therefore systemic evaluation is required to consider the association with BRBNS.
Subject(s)
Adult , Female , Humans , Arm , Blister , Colonoscopy , Diagnosis , Exophthalmos , Gastrointestinal Tract , Hemangioma , Hemangioma, Cavernous , Liver , Orbit , Rubber , Skin , Visual AcuityABSTRACT
PURPOSE: To evaluate the safety and efficacy of Medpor(R) SST(TM). The implant is composed of porous polyethylene with a smooth anterior surface with pre-drilled suture tunnels (SST) for attachment of extraocular muscles. METHODS: METHODS: Eight patients undergoing enucleation surgery received the unwrapped Medpor(R) SST(TM) orbital implant between August 2001 and December 2001. For each patient, data was acquired regarding complications, socket appearance and motility. RESULTS: Patients have been followed for 11 to 15 months. Socket healing was uneventful with no evidence of implant extrusion or migration. The socket motilities were better than grade 3 in all cases. The motilities of the prosthesis were grade 2 without peg insertion. CONCLUSIONS: The Medpor(R) SST(TM) orbital implant appears to be safe and to offer advantages over conventional implants.
Subject(s)
Humans , Muscles , Orbital Implants , Polyethylene , Prostheses and Implants , SuturesABSTRACT
Myiasis is most prevalent in Mexico, central and south America, tropical Africa, and the southwestern United States. Although dermal myiasis is rare in most of the United States, it is a disorder that may be seen in international travelers. In the United States, external myiasis is usually caused by the cattle botfly. We report here a case of ophthalmomyiasis involving the left upper eyelid of a child. We examined a six-year-old boy who presented to the Massachusetts Eye and Ear Infirmary (MEEI) in September 1998. He complained of persistent swelling of his left upper eyelid for the previous ten days. The edema and erythema were unresponsive to warm compresses and oral antibiotics. Ocular examination revealed a mild preseptal cellulitis of the left upper eyelid with a small draining fistula. On slit-lamp examination, we found one larva protruding intermittently from the fistula site. The larva was extracted with forceps, wrapped in a moist towel and sent in a jar to the parasitology laboratory. The specimen was identified as a Cuterebra larva by a parasitologist at the Harvard School of Public Health. One week later, the patient's eyelid edema and erythema had completely resolved.