Primary Amyloidosis of the Bladder / 대한비뇨기과학회지

Amyloidosis is a systemic disease characterized by the deposition of homogenous, eosinophilic and hyaline protein. Most cases of amyloidosis occur as a systemic disease, with a poor prognosis. Conversely, primary localized amyloidosis of the bladder has an excellent prognosis in most cases, it is, therefore, important to distinguish primary localized from systemic amyloidosis. Primary localized amyloidosis of the bladder is a rare disease, causing hematuria, which is often confused with bladder cancer. The diagnosis is usually made from a biopsy and subsequent pathological examination. We report a case of primary localized amyloidosis of the bladder, occurring in a 73 year old man, treated with a transurethral resection.

A Case of Systemic Lupus Erythematosus Presented as Pseudotumor Cerebri Syndrome / 대한류마티스학회지

Pseudotumor cerebri syndrome is characterized clinically by raised intracranial pressure without ventriculomegaly. Several conditions known to interfere with CSF absorption pathways at the level of the arachnoid villi can produce the pseudotumor cerebri syndrome. Systemic lupus erythematosus (SLE) is an autoimmune, inflammatory and chronic disorder characterized by multi-organ involvement including the nervous system. Clinical evidence of central nervous system involvement includes headache, seizure, psychosis and altered mental status. However, pseudotumor cerebri syndrome has been reported infrequently as a primary feature of central nervous system involvement or a complication of SLE. A 19 year-old female was admitted with seizure preceded by headache and blurred vision. Ophthalmoscopic examination showed papilledema. The diagnosis of pseudotumor cerebri syndrome was confirmed by increased intracranial pressure(>550mmH2O) in the absence of any abnormal radiological findings of the brain. We described a 19-year-old girl whose first clinical manifestation was pseudotumor cerebri syndrome, which was diagnosed as SLE later. Therefore pseudotumor cerebri syndrome may be the part of the spectrum of clinical manifestation of SLE.

A Case of Systemic Lupus Erythematosus Presented as Pseudotumor Cerebri Syndrome / 대한류마티스학회지

Pseudotumor cerebri syndrome is characterized clinically by raised intracranial pressure without ventriculomegaly. Several conditions known to interfere with CSF absorption pathways at the level of the arachnoid villi can produce the pseudotumor cerebri syndrome. Systemic lupus erythematosus (SLE) is an autoimmune, inflammatory and chronic disorder characterized by multi-organ involvement including the nervous system. Clinical evidence of central nervous system involvement includes headache, seizure, psychosis and altered mental status. However, pseudotumor cerebri syndrome has been reported infrequently as a primary feature of central nervous system involvement or a complication of SLE. A 19 year-old female was admitted with seizure preceded by headache and blurred vision. Ophthalmoscopic examination showed papilledema. The diagnosis of pseudotumor cerebri syndrome was confirmed by increased intracranial pressure(>550mmH2O) in the absence of any abnormal radiological findings of the brain. We described a 19-year-old girl whose first clinical manifestation was pseudotumor cerebri syndrome, which was diagnosed as SLE later. Therefore pseudotumor cerebri syndrome may be the part of the spectrum of clinical manifestation of SLE.