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Indian J Pediatr ; 2007 Oct; 74(10): 959-61
Article in English | IMSEAR | ID: sea-78571

ABSTRACT

Allgrove syndrome consists of triad of Adrenal hypoplasia, Achalasia cardia and Alacrimia. Often the first manifestation of adrenal hypoplasia is Addisonian crisis precipitated by infection or trauma. We present case of a 9-year-old boy who presented in shock due to adrenal failure later confirmed to have Allgove syndrome.


Subject(s)
Addison Disease/diagnosis , Child , Diagnosis, Differential , Drug Administration Schedule , Esophageal Achalasia/diagnosis , Humans , Hydrocortisone/administration & dosage , Lacrimal Apparatus Diseases/diagnosis , Male , Syndrome
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