Solitary infantile myofibromatosis of the orbit

Infantile myofibromatosis [IM] is an extremely rare cause of skull lesion in the new-born and paediatric population. The prognosis is related to the number of lesions and the presence or absence of visceral involvement. The authors report a case of IM, in a 5-year-old boy with an osteolytic lesion in the right orbital roof, which displaced the globe downwards. A subfrontal approach was made with total resection. The globe had regained a normal position and further evaluation revealed no other lesions. The patient's age at presentation, physical findings, radiographic appearance and the histopathological examination of the lesion are needed to generate a-differential diagnosis and to formulate a treatment plan