1.
Bol. Asoc. Méd. P. R
;
79(8): 325-8, ago. 1987. tab, ilus
Article
in English
| LILACS
| ID: lil-77054
ABSTRACT
Pheochromocytoma is a rare tumor in childhood. Most patients present with sustained hypertension (80%), and 50% of these tumors are bilateral, multiple or extraadrenal. An increased familia incidence in the form of a single mendelian dominance is also noted in the pediatric age groups. We report an 11 years old girl who presented with paroxysmal hypertension and an extra-adrenal, midline pheochromocytomia in the region of the celiac axis. To our knowledge, this specific location has been reported in the literature only once. Diagnostic and therapheutic problemas arose as a consequence of its uncommon presentation and anatomic location