ABSTRACT
Individualized as a real anatomo-clinical entity in 1924 by Darier and Ferrand, the dermatofibrosarcoma protuberans is a rare cutaneous tumor of intermediate wickedness, which is characterized by its slow evolution, its local aggressiveness, a high power of recurrence and the rarity of metastases. Our casuistry lasts from february 2001 to october 2010 when 22 cases were supported. We distinguish 15 men and 7 women, whose average age was 42 years, ranging from 11 years to 64 years. Surgical excision of the tumor was large, with safety margins of 5 cm in 21 patients and 3 cm for a neck tumor. Of the 13 patients treated in first intention, none has recurred with a mean of 7 years. Other patients complain only one recurrence. None of our patients presented metastasis. The dermatofibrosarcoma mainly affects young adults with a slight male predominance. Its clinical diagnosis is difficult in the beginning stage, but he is more evident in the state phase. Histology, immunohistochemistry and the immunolabelling of the CD34 antigen, confirm the diagnosis. Different techniques can cover losses of substance caused by this mutilating surgery. Tumors are all of size greater than 5cm. Treatment is always surgical and must satisfy two principles: a wide margin of excision in the area and the sacrifice of a healthy anatomical barrier in depth