ABSTRACT
The dermatofibrosarcoma protuberans is a rare but not exceptional tumor of the skin. It is misdiagnosed, often after multiple surgical debulking with cosmetic damage. The authors report the case of a 59 years old woman presenting a voluminous dermatofibrosarcoma protuberans located in the parotid area and not associated with facial palsy and trismus. The treatment consisted in a large surgical debulking of the sarcomatous tumor, the covering skin and the superficial lobe of the parotid. The surgeon used local flaps to repair the cosmetic damage. The post operative follow-up was of 1 year without complications and recurrence. Dermatofibrosarcoma protuberans is a cutaneous tumor characterized by local malignancy. It is seen mainly in adults regardless to sex and it is rarely seen in head and neck. This tumor has a rare propensity to metastasise and high relapse and sarcomatous transformation rates, A large debulking is the only solution to avoid a local recurrence