Foix-chavany-marie syndrome [anterior opercular syndrome] case report

Foix-Chavany-Marie syndrome is a rare cortico-subcortical suprabulbar or pseudobulbar palsy of the lower cranial nerves 5, 7, 9, 10 and 12. This syndrome consists of anarthria, bilateralvolitional paresis of the facial, lingual, pharyngeal, and masticatory muscles bilaterally with preservation of the reflexive, emotional and autonomic innervations of the same muscles. We present the first case report in the Middle East of Foix-Chavany-Marie syndrome

Uncommon incidental pseudoaneurysm. Diagnostic and management challenges

To analyze patients with uncommon incidental pseudoaneurysms, secondary to non-catheterization causes, and to discuss the peculiar clinical spectrum, and focus on some aspects of difference from post-catheterization pseudoaneurysms. Eleven patients, 8 males and 3 females, were studied retrospectively in Jordan University Hospital, Amman, Jordan, between 2002-2008. Radiological studies performed included duplex sonography [DS], computed tomography [CT], conventional angiography, magnetic resonance imaging [MRI], and magnetic resonance angiography [MRA]. Pseudoaneurysms were most commonly encountered in young males [63.6%], especially in the lower limb vessels [36%]. Clinical findings were suggestive of pseudoaneurysms in 27% of our cases. Four out of the 8 DS scans showed the neck of pseudoaneurysms, and the "to and fro" waveform, the strongest indicators for pseudoaneurysms. Both CT with intravenous contrast and angiography failed to establish the diagnosis in one out of 5 cases. The MRI with MRA showed the pseudoaneurysms in 2 patients that underwent the scan. Incidental pseudoaneurysms are considered following iatrogenic procedures, penetrating, or blunt traumas with variable delay time. Young healthy males are at increased risks, as opposed to elderly females with calcified vessels in post-catheterization cases. Duplex sonography is less sensitive in incidental than post-catheterization pseudoaneurysms. The CT scan with intravenous contrast has high accuracy in establishing the diagnosis in small, or medium sized pseudoaneurysms. The MRI and MRA are accurate valuable studies and comparable to conventional angiography

Bilateral renal angiomyolipoma with bilateral sarcomatous change

A 54-year-old man presented to the nephrology clinic with three months history of hematuria, weight loss and loss of appetite. Radiological and pathological investigations pointed to the diagnosis of multiple bilateral renal angiomyolipomas with bilateral high grade sarcomatuos transformation and lung metastasis, and with no manifestations of tuberous sclerosis. This is the first reported case of bilateral renal angiomyolipomas with multiple sarcomatous changes