[Fanconi anemia complicated by neutropenic enterocolitis]

Neutropenic enterocolitis [NEC] also known as typhlitis is an acute, life-threatening inflammation of the small and large bowel often seen in patients with leukaemia undergoing cytotoxic chemotherapy; occasionally this syndrome could present in other immunocompromised patients. To report an unusual case of fanconi anemia complicated by neutropenic enterocolitis. We report a case of a 13-year-old boy affected by Fanconi anemia with severe neutropenia and who presented Neutropenic enterocolitis. Abdominal ultrasonography showed thickening of cecum and ascending colon of 1.18cm. The outcome was favourable with medical management. Neutropenic enterocolitis in Fanconi anemia is a rare and a severe illness; however the outcome is improved with early management

[Cholangitis reveling an intrahepatic Osler's disease]

Osler Weber Rendu Disease is a hereditary haemorrhagic telangectasia habitually revealed by reccurent bleeding [epistaxis]. Hepatic involvement in Osler disease is found in 8 to 31%, manifested by cholestasis. We report an original observation of a cholangitis revealing Osler disease