ABSTRACT
Pulmonary sequestration and congenital cystic adenomatoid malformation are infrequent congenital lung disease and the combination of these two entities is rare. Here a case of left pulmonary sequestration with congenital cystic adenomatoid malformation in an asymptomatic elderly woman who presented with recent massive haemoptysis is reported. Fine needle aspiration cytology showed hypercellularity with micro-acinar pattern and mild pleomorphism. Computerised tomography scan depicted a round mass with rim of peripheral enhancement at left lower lobe of the lung. Intra-operative findings were suggestive of an intralobar sequestration with multiple aberrant vascularisation. Histologically intralobar sequestration was associated with congenital cystic adenomatoid malformation and epithelial atypia.