ABSTRACT
Double outlet left ventricle [DOLV] is a rare but substantial congenital cardiac anomaly, presenting with varied anatomical findings. This requires a relevant surgical approach, pertinent to the type of presentation. The condition can be quite difficult to diagnose. This implies the need for scrutiny and sensitive diagnostic procedures during the pre-op period. The case presented here was in a critical state on admission and was stabilised with Sildenafil during the pre-op preparation. A surgical plan for Arterial Switch was made, keeping in mind the diagnosis suggestive of TGA, VSD with an AP Window at first. DOLV was confirmed on the operating table and Rastelli type of correction was performed with a relatively uneventful stay in the post-op ICU
ABSTRACT
Anomalous origin of the left coronary artery from the pulmonary artery also recognized as Bland White Garland syndrome is a very rare congenital condition. A two-months old baby boy presented with dyspnoea for two weeks and a pansystolic murmur on auscultation. The base line investigations showed cardiomegaly and bilateral basal haze on X-ray chest. ECG showed ST elevation in leads I and AVI and echocardiography showed situs solitus, levocardia, hypokinetic intra-ventricular septum, ejection fraction of 30%, mitral regurgitation of grade-I and an anomalous origin of the left coronary artery from pulmonary artery was diagnosed. Patient was in left heart failure. It was rectified surgically by creating a trans-pulmonary tunnel [Takeuchi repair]. Postoperative course was uneventful and he was finally discharged in stable condition