ABSTRACT
A fifty-three-year-old Bahraini male presented with a painless, slow growing mass in the left gluteal region. A work-up including pelvic MRI, chest CT scan and excisional biopsy was performed. The histology was low-grade fibromyxoid sarcoma [LGFMS]. Immunohistochemistry tests confirmed the diagnosis. He received local radiotherapy as an alternative for re-resection. Changes in the liver were suspicious but an ultrasound and MRI of the liver ruled out liver metastases. The patient is maintained under close observation because the tumor has high tendency of local recurrence and possible pulmonary and liver metastases. This specific distinctive entity of soft tissue sarcoma is yet to be reported in Bahrain; it has no clear protocol regarding the best follow-up recommendations.