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Arch. argent. dermatol ; 65(4): 140-143, jul.-ago. 2015. ilus
Article in Spanish | LILACS | ID: biblio-848996

ABSTRACT

El pénfigo familiar benigno (Enfermedad de Hailey-Hailey) es una rara genodermatosis localizada en pliegues, que cursa en brotes con ardor y prurito localizado predominantemente en verano. Presentamos dos pacientes con Enfermedad de Hailey-Hailey de diagnóstico tardío(AU)


Benign familial pemphigus (Hailey-Hailey disease) is a rare genodermatosis located in folds, which presents in outbreaks with burning and itching predominantly in summer. Two patients with Hailey-Hailey disease of late diagnosis are reported (AU)


Subject(s)
Humans , Male , Female , Adult , Pemphigus, Benign Familial/diagnosis , Adrenal Cortex Hormones/therapeutic use , Calcineurin Inhibitors/therapeutic use , Diagnosis, Differential , Pemphigus, Benign Familial/pathology , Therapeutics
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