ABSTRACT
This article deals with the extra skeletal mesenchymal chondrosarcoma especially the muscular localisation, through a report of one case and review of literature. It concerns a 38 years old female patient who developed a muscular tumor in her right calf, since 18 months. Treated by wide surgical resection without any adjuvant treatment. Follow up for 6 years showed a good general condition and no signs of local recurrence or distal metastasis. The extra skeletal mesenchymal chondrosarcoma exceptionally affects young patients. Treatment is essentially surgical. Radiotherapy and chemotherapy do not prove their efficiency. Local recurrence rate is about 52% in the subsequent 2 years, that is why a very rigorous surveillance should be done in this period. prognosis is bad wirh a 10 years survival rate of 32%