[Soft tissue alveolar sarcoma: Study of two cases with bones envolvement]

We report two cases of alveolar soft part sarcoma associated with bone involvement. The first case concerned a 61-year old female patient with a left sus-clavicular mass and the second a 67-year old male patient with a tumor of the left hand. The bone involvement, observed on skeletal radiography, was histologically confirmed. Surgery was the treatment in both cases, followed by radiotherapy in one case. Alveolar soft part sarcoma is a rare soft tissue malignant tumor with a local slowly growing and pejorative prognosis. If metastasis of lung, brain and bone are often present at diagnosis, the local bone involvement is not well documented

Solar risk and sun protection in adolecents

Several studies proved that sunrays intense exposure, since childhood, is a primordial environment factor which increases risk of melanoma. The aim of this study is to evaluate the knowledge of a group of students concerning the consequences of sun exposure, and to insist on the importance of information and prevention. Method: a survey was conducted on a sample of 1000 students in several schools of Casablanca. A questionnaire with 21 items with open answers was auto-filled by all the participants. there were 66,6% girls and 33,4% boys, with a mean age of 13 year-old. 38% of girls and 24% of boys were frequently exposed to the sunrays. The time of exposure was between midday and 4pm. 16% of the students knew that it is the maximal luminal intensity and requires maximal sun protection. The frequency of sunburns was high [43% of girls / 34% of boys]. Most of them exposed themselves regularly at the highest risk hours. The use of external solar photo protector was less frequent when practicing sport [16% of girls and 7% of boys]. During sport, 13% of the students knew the need to renew the application every two hours or after the bath. 54% of girls and 45% of boys knew that the clothes are the best protection.This study shows that the risk of sun exposure is badly known within teenagers and it exists a misreading of the benefit of sunscreen and of the role of clothes. Information, education of children and their families and the awareness of doctors about the solar risk are the best way to eliminate the high increase of the bad effects of the sun [melanoma, hyperpigmentation]

Lupus erythematosus with revealing dermatitis in children: a 26 cases report

The infant lupus erythematosus is rare before the age of 15 years and exceptional during the first 2 years of life. Through a retrospective study of 26 child lupus erythematosus collected in Casablanca Ibn Rochd Dermatology Unit from January 1970 to December 2002, we tried to study anamnestic, clinical, paraclinical, therapeutic and evolutive characteristics of this disease in our context. The children were 7 day-old to 15 year-old with a mean age of 12 years and a clear female predominance [76.9%]. The cutaneous manifestations were the first symptom in all cases. The extracutaneous manifestations were detected in 10 cases [38.46%]. The anatomic clinical forms were: chronic lupus erythematosus in 13 cases, systemic lupus erythematosus in 9 cases, subacute lupus erythematosus in 2 cases, deep lupus erythematosus in one case, neonatal lupus erythematosus in one case. Treatment of the systemic lupus was corticotherapy in 10 cases. In pure dermatologic forms, dermocorticoids were given to 10 children and synthesis antimalarial to 3 children. The remission was obtained in 15 cases [57.69%] and 3 had relapses. Our study showed the predominance of the child lupus erythematosus in girls, the diversity of the clinical forms in this age with predominance of the chronic lupus erythematosus

Juvenile dermatomyositis: a 8 cases report

Juvenile dermatomyositis is a multisystemic rheumatic disorder characterized by non infectious inflammation of skin and striated muscle. The aim of this retrospective study is to stress the diagnostic and therapeutic difficulties of dermatomyositis in children. From January 1990 to December 2002, 8 cases of childhood dermatomyositis were collected in the Dermatology Department of Casablanca University Hospital. The mean age of our patient was 10 year-old [3 to 14 year-old]. They were 6 girls and 2 boys. The evolution mean duration was 17 months. Cutaneous and muscular signs were found in all cases. Raynaud's phenomenon was present in 2 cases. Two children had bad general status and 1 child had a dysphagia. An inflammatory syndrome was present in all cases. Muscle enzymes were increased in 6 patients [75%]. Muscular biopsy has confirmed the diagnosis in 5 cases [62%]. High dose corticosteroid therapy was used in all cases, associated to immunosuppressive therapy in 1 case. The evolution was good in 2 cases. Three children had a relapse with cutaneous calcinosis in 2 cases. Three patients were lost from follow-up. Juvenile dermatomyositis is a severe disease. Corticosteroids, associated to immunosuppressors or immunoglobulins have decreased mortality. The prognosis depends on an early diagnosis and treatment

[Xeroderma Pigmentosum [176 cases]]

In a retrospective study of 176 cases of Xeroderma Pigmentosum collected at the Dermato-Venerology department of University Hospital lbn Rochd of Casablanca, during a period of 22 years, we have noticed the following data :man predominance is slight [61.9%], the average age at the first consultation is advanced [6 years] patient's parents consanguinity is observed in 54.5%. Cutaneous abnormalities are the main clinical features :poikilodderma [100%] and cutaneous tumors [81.1%]. Ocular involvement is present in 55.7% where as neurologie involvement is noted only in 6.8%. For all the patients, protection from sun exposure and various treatments for cutaneous tumors were not sufficient to avoid dramatic follow-up with 80% of mortality at fifteen