A Case of Hellermann-Streiff Syndrome

Hallermann-Streiff Syndrome is a rare congenital anomaly characterized by dyscephalia, dental anomalies, hypotrichosis, congenital cataract, bilateral microphthalmia and has characteristic feature of bird face due to marked mandibular hypoplasia and beaked nose. The authors have experienced a case of Hallermann-Streiff Syndrome combined with bilateral aphakia and glaucoma in a 34 years old woman and we report this case with the review of literatures.

A Clinical Study of Industrial Ocular Injuries

The authors clinically analysed 317 industrial ocular injuries among 16,466 patients who visited department of ophthalmology of Masan Koryo General hospital during the 5 years from January 1, 1982 to December 31, 1986. The results were as follows: 1. The ambulation rate of industrial ocular injuries was 1.9% of all eye patients and 18.4% of all industrial injuries. 2. The incidence was higher in male(95.6%) and in the age of 3 rd decade(5.2%). 3. The incidence of affected side was 54.0% on the right, 37.5% on the left, and 8.5% on both sides. 4. There was no significant differences in seasonal distribution. 5. The most common cause of industrial ocular injuries was iron piece(32.8%) as a flying particle, followed by wire and nail(15.1%) and chemicals(8.2%). 6. Corneal foreign body(15.8%) was the most common disease of all industrial ocular injuries, followed by corneal laceration(12.7%) and thermal burn, conjunctiva and cornea(8.9%). 7. 29.3% of all industrial ocular injuries were hospitalized. Corneal laceration(21.0%) was the most common disease among in-patients and surgical procedures in in-patients included corneal suture(33.0%), lens extraction(17.5%), corneosclecral suture(13.6%). The average duration of hospitalization was 16.8 days. 8. The average duration of treatment required for all industrial ocular injuries was about 46.3 days. 9. The final visual acuity was improved to 0.9 or more in 45.3% and 34 eyes(9.9%) were below 0.1. 10. The most common complication of industrial ocular injuries after treatment was traumatic cataract(18.4%), followed by corneal opacity(16.8%) and irregular astigmatism(14.4%).

A Case of Acute Posterior Multifocal Placoid Pigment Epitheliopathy, Associated with Bilateral Serous Retinal Detachment

Acute posterior multifocal placoid pigment epitheliopathy(APMPPE) was first described by Gass in 1968. This syndrome is characterized by sudden loss of central vision secondary to multifocal yellowish-white placoid lesion of posterior pole at the level of the pigment epithelium and significant visual improvement after spontaneous resolution within a few weeks. In the early arterial and arteriovenous phase of fluorescein angiography, choroidal fluorescence is blocked by the placoid lesion but becomes hyperfluorescent in the late venous phase due to staining of the lesion. We experienced and treated a case of acute posterior multifocal placoid pigment epitheliopathy associated with bilateral serous retinal detachment in 29 years old male patient, who had a good visual improvement.

A Case of Acute Posterior Multifocal Placoid Pigment Epitheliopathy, Associated with Bilateral Serous Retinal Detachment

Acute posterior multifocal placoid pigment epitheliopathy(APMPPE) was first described by Gass in 1968. This syndrome is characterized by sudden loss of central vision secondary to multifocal yellowish-white placoid lesion of posterior pole at the level of the pigment epithelium and significant visual improvement after spontaneous resolution within a few weeks. In the early arterial and arteriovenous phase of fluorescein angiography, choroidal fluorescence is blocked by the placoid lesion but becomes hyperfluorescent in the late venous phase due to staining of the lesion. We experienced and treated a case of acute posterior multifocal placoid pigment epitheliopathy associated with bilateral serous retinal detachment in 29 years old male patient, who had a good visual improvement.