ABSTRACT
Neurofibromatosis type 1 (von Recklinghausen disease, NF1) involves the central and peripheral nervous systems as well as the skin, bone, endocrine, gastrointestinal and vascular systems. The gastrointestinal neurofibroma associated with NF1 has been infrequently reported. We report our experience with a 15-year-old boy who had a gastric plexiform neurofibroma with upper gastrointestinal bleeding and underwent a tumorectomy because of massive upper gastrointestinal bleeding. We conclude that gastrointestinal bleeding and anemia in the setting of NF1 mandates complete endoscopic examination of the digestive tract to rule out neurofibromas. Surgical resection is the standard treatment.
Subject(s)
Adolescent , Humans , Male , Anemia , Gastrointestinal Tract , Hemorrhage , Neurofibroma , Neurofibroma, Plexiform , Neurofibromatoses , Neurofibromatosis 1 , Peripheral Nervous System , Skin , StomachABSTRACT
Congenital left ventricular aneurysm is rare, poorly understood, and potentially lethal. Also, congenital coronary artery fistula is rare but hemodynamically, it induces myocardial ischemia due to coronary steal syndrome and diastolic volume overload from a left to left shunt. A 64-year-old women with abnormal ECG and mild exertional dyspnea was admitted to our hospital for further evaluation. Electrocardiography demonstrated Q waves, inverted T waves in the inferior leads and right bundle brach block. Transthoracic electrocardiography showed left ventricular septal aneurysm. Cardiac catheterization, a selective left coronary arteriogram revealed a fistula. The fistula originated from the proximal portion of the left anterior descending coronary artery and drained into the left ventricle. Magnetic resonance imaging demonstrated congenital defect muscular portion of interventricular septum. Thallium 201 heart spect showed regional perfusion defect along the inferior-lateral segment of the left ventricle. Then we report an congenital left ventricular septal aneurysm associated with coronary fistula.
Subject(s)
Female , Humans , Middle Aged , Aneurysm , Cardiac Catheterization , Cardiac Catheters , Congenital Abnormalities , Coronary Vessels , Dyspnea , Electrocardiography , Fistula , Heart , Heart Ventricles , Magnetic Resonance Imaging , Myocardial Ischemia , Perfusion , Thallium , Tomography, Emission-Computed, Single-PhotonABSTRACT
Congenital left ventricular aneurysm is rare, poorly understood, and potentially lethal. Also, congenital coronary artery fistula is rare but hemodynamically, it induces myocardial ischemia due to coronary steal syndrome and diastolic volume overload from a left to left shunt. A 64-year-old women with abnormal ECG and mild exertional dyspnea was admitted to our hospital for further evaluation. Electrocardiography demonstrated Q waves, inverted T waves in the inferior leads and right bundle brach block. Transthoracic electrocardiography showed left ventricular septal aneurysm. Cardiac catheterization, a selective left coronary arteriogram revealed a fistula. The fistula originated from the proximal portion of the left anterior descending coronary artery and drained into the left ventricle. Magnetic resonance imaging demonstrated congenital defect muscular portion of interventricular septum. Thallium 201 heart spect showed regional perfusion defect along the inferior-lateral segment of the left ventricle. Then we report an congenital left ventricular septal aneurysm associated with coronary fistula.
Subject(s)
Female , Humans , Middle Aged , Aneurysm , Cardiac Catheterization , Cardiac Catheters , Congenital Abnormalities , Coronary Vessels , Dyspnea , Electrocardiography , Fistula , Heart , Heart Ventricles , Magnetic Resonance Imaging , Myocardial Ischemia , Perfusion , Thallium , Tomography, Emission-Computed, Single-PhotonABSTRACT
A totally implanted venous access system was inserted in 19 children with cancer. The devices were utilized for the administration of antineoplastic drugs, parenteral fluids, antibiotics, and blood products. Total duration of implantation was 4,046 days for 23 implanted system (range 7-445 days). Complications included cather infection (0.247/100 catheter days), occlusion (0.692/100 catheter days), and dislodgement of needle (0.643/100 catheter days). There were major complications that necessitated removal of catheters, including systemic infections (0.09/100 catheter days) and complete occlusions (0.09/100 catheter days). The system was thought to be safe and convenient in chemotherapy, and permitted full physical activity.