[A case of long QT syndrome]

Congenital long-QT syndrome is infecting a form of anomaly characterized by prolongation of cardiac repolarization with a prolonged QT interval on the Scalar ECG and a tendency to develop polymorphic ventricular tachycardia which in itself may change into ventricular fibrillation. Because of the importance of its diagnosis and steps necessary to prevent sudden cardiac death, acknowledge about its clinical and Para clinical presentation seems essential. In this article, a case of long QT Syndrome in a 14 year old boy without a history of any disease in the past is reported who eventually underwent ICD + pacing implantation