ABSTRACT
Conus medullaris ganglioglioma is rare and an usually benign tumour. Ganglioglioma may occur anywhere in the cranio-spinal axis but is rarely encountered in the spinal cord. It is observed more in the younger age group. Symptoms and signs are usually long and variable. Since this condition is rare it is easily overlooked and mistakenly diagnosed. When removed entirely the outcome is favourable. We report a 5-year-old boy who presented with a 3-year history of unsteady gait and lower limbs deformity, it was initially confused with congenital bone anomalies. His condition worsened over the following 6 months before his imaging scans identified a mass lesion involving the conus medullaris with syringomyelia. He underwent gross total removal of the tumour and the histopathology identified clusters of ganglion and glial cells. He made an excellent neurological recovery