ABSTRACT
Papillon Lefevre Syndrome is a rare syndrome autosomal recessive in nature, manifesting as keratosis palmoplantaris with periodontitis. A case of Papillon Lefevre Syndrome present in a 12 year old boy is presented. Only the permanent maxillary canines were present in the oral cavity when the patient was first seen, and despite efforts towards preservation, they had to be extracted. (complete dentures were made and the patient was followed up for 26 months.
Subject(s)
Alveolar Bone Loss/etiology , Child , Denture, Complete , Follow-Up Studies , Humans , Male , Papillon-Lefevre Disease/genetics , Periodontal Diseases/etiology , Tooth Loss/etiology , Tooth Mobility/etiologyABSTRACT
Supernumerary or extra teeth result from disturbances during the initiation and proliferation stages of dental development. Teeth formed in excess of the normal number are termed supernumerary teeth. A supernumerary tooth may closely resemble the teeth of the group to which it belongs i.e. molars, premolars or anterior teeth or it may bear little resemblance in size or shape to the teeth with which it is associated. Discussed here are reports of three cases with multiple supernumerary teeth in the mixed dentition and its management.