ABSTRACT
Retinitis pigmentosa has been recognized as a symmetrical, bilateral, hereditary, tapetoretinal degeneration with night blindness, visual field loss, and abnormal ERG. Unilateral retinitis pigmentosa is a rather rare disease. Pedraglia described first reported a case of suspected unilateral retinitis pigmentosa in 1865. Francois and Verriest proposed the following four criteria of the unilateral retinitis pigmentosa: the presence of functional changes ophthalmoscopically typical primary pigmentary degeneration in the affected eye, the absence of a tapetoretinal dystrophy in the fellow eye with normal ERG over five years and exclusion of the inflammatory cause in the affected eye. We report a case of unilateral retinitis pigmentosa in 29 year-old female who has been followed for over five years.