Congenitally corrected transposition of the great arteries:anatomic repair or fontan pathway? / 中华胸心血管外科杂志

Objective To review the early-and mid-term results of anatomic repair or Fontan pathway for congenitally corrected transposition of the great arteries(ccTGA) in a single institution of China.Methods Hospital records over a 9-year period(2009-2017) were reviewed to identify patients with ccTGA who underwent anatomic repair or Fontan pathway.Pa-tient-and procedure-related variables were reviewed.Results We identified 37 patients.Group 1 consisted of 10 anatomic re-pairs, of which 4 required prior pulmonary artery banding.Median age at anatomic repair was 1.0 years( range: 0.3 -7.8 years).There was one early death, and one patients experienced ECMO support.The mean follow-up was(3.0 ±2.8)years (range:0.7-8.4 years).Five(55.5％) patients showed arrhythmias, and one required permanent pacemaker implantation during follow-up.Group 2(27 patients) underwent Fontan palliation, of which 23(85.2％) underwent prior bidirectional Glenn shunt.Median age at Fontan completion was 3.8years(range:2.2-14.3 years).there was one early death with a mor-tality of 3.7％.The mean follow-up was(2.8 ±1.6) years(range:0.8-8.2 years).There was 4(15.4％) cases of arrhyth-mias, but none required reintervention.The arrhythmias incidence in Fontan group was significantly lower than the anatomic re-pair group.The early-and mid-term survival rate were 90.0％ and 96.3％in the two groups.The difference was not statistical-ly significant(P=0.458).Conclusion Patients with ccTGA do well with both anatomic repair and the Fontan pathway in the medium term.Pulmonary artery banding can be used effectively for morphological left ventricular retraining , and extenuate tri-cuspid regurgitation.Excellent outcomes with reduced early complication and arrhythmias incidence can be achieved for this co-hort of patients when a strategy of avoiding complex anatomic repair in favor of the Fontan pathway is used .

Anatomical repair of a bilateral Tessier No. 3 cleft by midfacial advancement / 대한악안면성형재건외과학회지

BACKGROUND: Bilateral Tessier number 3 clefts are extremely rare, and their surgical treatments have not been well established. CASE PRESENTATION: The authors describe the case of a patient with a right Tessier number 3, 11 facial cleft with microphthalmia, a left Tessier number 3 facial cleft with anophthalmia, and cleft palate. We repaired simultaneously the bilateral soft tissue clefts by premaxillary repositioning, cleft lip repair, facial cleft repair by nasal lengthening, midfacial advancement, and an upper eyelid transposition flap with repositioning both the medial canthi. Postoperatively, the patient showed an esthetically acceptable face without unnatural scars. CONCLUSIONS: We achieved good results functionally and esthetically by midfacial advancement with facial muscle reposition instead of traditional interdigitating Z-plasties. The surgical modality of our anatomical repair and 3 months follow-up results are presented.

Clinical Outcomes after Anatomic Repair Including Hemi-Mustard Operation in Patients with Congenitally Corrected Transposition of the Great Arteries

BACKGROUND AND OBJECTIVES: The aims of this study were to determine the early and late outcomes of anatomic repair of congenitally corrected transposition of the great arteries (ccTGA) and to evaluate effectiveness of the hemi-Mustard procedure. SUBJECTS AND METHODS: We conducted a retrospective, single-center study of patients who underwent anatomic repair for ccTGA between July 1996 and December 2013. Sixteen patients were included in the study. The median age at the time of the operation was 3.5 years (range: 0.5-29.7), and the median body weight was 13.3 kg (range: 5.8-54). The median follow-up duration was 7.7 years (range: 0.2-17.4). RESULTS: Atrial switch was achieved using the Mustard procedure in 12 patients (hemi-Mustard procedure in 11) or the Senning procedure in four patients. The ventriculoarterial procedure was performed using the Rastelli procedure in 11 patients and arterial switch in five patients. Six patients underwent tricuspid valvuloplasty. The survival rate was 93.8±6.1%. The rate of freedom from reoperation at 5 years was 92.3±7.4% in the Rastelli group. All patients except one were New York Heart Association class I. All patients except one had mild tricuspid regurgitation. CONCLUSION: Anatomic repair can be performed with a low risk of in-hospital mortality. The hemi-Mustard strategy for selected patients is one solution for reducing early mortality and morbidity, and long-term complications such as venous pathway stenosis or sinus node dysfunction.

Reparos anatómicos del origen del músculo supinador y sus implicaciones en el tratamiento del dolor lateral de codo / Anatomical Repair of the Supinator Muscle Origin and Its Implications in the Treatment of Lateral Elbow Pain

Introducción: en el tratamiento quirúrgico de la epicondilitis se han descrito varios procedimientos encaminados a resecar el origen del extensor carpi radialis brevis (ECRB). Un porcentaje de pacientes que reciben tratamiento quirúrgico continúa con dolor, siendo una posible causa la compresión del nervio interóseo posterior. Objetivo: describir el origen de las cabezas superficial y profunda del músculo supinador y la relación entre estas y el origen del ECBR a nivel del epicóndilo lateral. Métodos: disección de 18 codos de cadáveres frescos. Se disecaron los músculos que tiene origen en el epicóndilo lateral, con énfasis en las cabezas superficial y profunda del músculo supinador y su relación con el origen del ECRB y el ligamento colateral lateral ulnar (LCLU). Resultados: los orígenes de las cabezas superficial y profunda del músculo supinador son adyacentes entre sí, pero diferentes, en íntima relación con el origen de ECRB. La cabeza profunda se origina en la base del epicóndilo lateral superior al ecuador del capitellum, anterior al origen del ECRB. La cabeza superficial se origina en la base del epicóndilo lateral de 2 a 4 mm antero inferior al origen del ECRB y en la longitud del LCLU. Conclusiones: la relación anatómica del origen de las cabezas superficial y profunda del músculo supinador con el origen del ECRB y el LCUL, permitirían realizar su resección concomitante con la resección del ECRB en el tratamiento de la epicondilitis de manera segura(AU)

Introduction: several procedures are described in the epicondylitis surgical treatment to resect the origin of the carpi radialis brevis extensor. It is still painful for a percent of patients who receive surgical treatment. The compression of the posterior interosseous nerve is a possible cause. Objective: describe the origin of the superficial and deep heads of supinator muscle and the relationship between them and the origin of carpi radialis brevis extensor at lateral epicondyle. Methods: dissection of 18 fresh corpses elbows. The muscles that originate from the lateral epicondyle were dissected, emphasizing on the superficial and deep heads of supinator and its relation to the origin of carpi radialis brevis extensor and the lateral ulnar collateral ligament. Results: the origins of the superficial and deep heads of supinator are adjacent to each other but different, closely related to the origin of carpi radialis brevis extensor. Deep head originates at the base from the superior lateral epicondyle to the capitellum Ecuador, before the origin of carpi radialis brevis extensor. Head surface originates at the base of lateral epicondyle 2 to 4 mm below the origin of the anterior and carpi radialis brevis extensor and in the length of the lateral ulnar collateral ligament. Conclusions: the anatomical relationship of the origin of the superficial and deep heads of supinator to the origin of carpi radialis brevis extensor and lateral ulnar collateral ligament would allow for concomitant resection of the carpi radialis brevis extensor safely resection in the treatment of epicondylitis(AU)