ABSTRACT
@#Caudal Duplication Syndrome is a rare case, congenital anomalies, involved the alimentary tract duplications and urogenital tracts duplication. The incidence is 1:100.000 births. We present a case of two months old female baby with abnormal genitalia and imperforate anus related to caudal duplication syndrome. On physical assessment we found duplication of vagina with single uterus and urethra with anorectal malformation (anovestibular and rectovaginal type). Intraoperative findings showed double-duplication of ascending colon, transverse, descending and half of sigmoid with duplication of the rest of sigmoid and rectum; left-sided rectum was adjacent to left vestibule and right-sided rectum adjacent to the right vagina; duplication of bladder and urethral duplication. On fourth, the reconstruction surgery was performed to correct digestive abnormality with Posterior Sagittal Anorectoplasy (PSARP) and separating duplication segment using stapler. Stapler was enough to separate duplication. Further reconstructive surgery were needed to achieve better gastrointestinal and genitourinary function outcome.
ABSTRACT
Anorectal duplications account for only 5% of gastrointestinal duplications, and cases with involvement of the anal canal are much rarer. Nearly all anorectal duplications are posterior to the rectum; duplications located anterior to the normal rectum are highly unusual, and only a few cases have been reported. We report the case of an anterior anorectocolonic duplication presenting as a rectovaginal fistula in a 2-month-old infant. After diagnosis, the duplication was excised completely without further intestinal complications.
Subject(s)
Humans , Infant , Anal Canal , Diagnosis , Fistula , Rectovaginal Fistula , RectumABSTRACT
Complete colonic duplication is a very rare congenital anomaly that may have different presentations according to its location and size. Complete colonic duplication can occur in about 15% of all gastrointestinal duplications. Double termination of tubular colonic duplication in the perineum is even more uncommon. We present a case of a Y-shaped tubular colonic duplication which presented with a rectovestibular fistula and a normal anus. Radiological evaluation and initial exploration for sigmoidostomy revealed duplicated colons with a common vascular supply. Endorectal mucosal resection of theduplicated distal segment till the colostomy site with division of the septum of the proximal segment and colostomy closure proved curative without compromise of the continence mechanism. Tubular colonic duplication should always be ruled out when a diagnosis of perineal canal is considered in cases of vestibular fistula alongwith a normal anus.
Subject(s)
Anal Canal , Colon , Colostomy , Diagnosis , Fistula , PerineumABSTRACT
Tubular colonic duplication presenting in adults is rare and difficult to diagnose preoperatively. Only a few cases have been reported in the literature. We report a case of a 29-year-old lady presenting with a long history of chronic constipation, abdominal mass and repeated episodes of abdominal pain. The abdominal-pelvic computed tomography scan showed segmental bowel wall thickening thought to be small bowel, and dilatation with stasis of intraluminal content. The provisional diagnosis was small bowel duplication. She was scheduled for single port laparoscopic resection. However, a T-shaped tubular colonic duplication at sigmoid colon was found intraoperatively. Resection of the large T-shaped tubular colonic duplication containing multiple impacted large fecaloma and primary anastomosis was performed. There was no perioperative complication. We report, herein, the case of a T-shaped tubular colonic duplication at sigmoid colon in an adult who was successfully treated through mini-laparotomy assisted by single port laparoscopic surgery.
Subject(s)
Adult , Humans , Abdominal Pain , Colon , Colon, Sigmoid , Congenital Abnormalities , Constipation , Dilatation , LaparoscopyABSTRACT
This paper introduced a case of colonal duplication before operation diagnosed by X-ray. The colonal duplication is rare benign congenital abnormality. The prognosis depends on the extent of lesion and combination of other abnormality. There are many ways of the treatment: tubular colonal duplication treated by stripping the mucosa, cyst colonal duplication treated by removal of cyst
Subject(s)
Adult , ColonABSTRACT
Segmental dilatation of small intestine is a rare form of the congenital intestinal anomaly. Many other congenital anomalies have been reported in these patients, but to our knowledge, the association with colonic duplication has not been reported in literatures. Herein we report a case of segmental dilatation of distal ileum associated with colonic duplication. The main clinical and pathogenic aspects are discussed, and the literatures were reviewed.