ABSTRACT
Se presenta una niña de 16 meses de edad, con una lesión de catorce meses de evolución que consistía en una única placa eritematosa, en forma de L, bien delimitada, localizada en la parte superior de la espalda. El signo de Darier fue positivo. La histopatología mostró edema intersticial y en la tinción con Giemsa, se observaron mastocitos. Se realizó el diagnóstico de un mastocitoma solitario. El mastocitoma solitario es una lesión tumoral benigna, que representa aproximadamente el 15% de la mastocitosis cutánea.
We report a 16 month years old female, with a 14 months history of a single erythematous, L shaped well-delimited plaque located on her upper back. Darier sign was positive. Histopathology revealed interstitial edema. The Giemsa staining showed mast cells. The diagnosis of a solitary mastocytoma was performed. Solitary mastocytoma is a benign tumoral lesion, that represents approximately 15% of cutaneous mastocytosis.
ABSTRACT
El mastocitoma solitario es la segunda en frecuencia, de las variantes de las mastocitosis, caracterizada por una proliferación de los mastocitos tisulares que afecta únicamente a la piel, comúnmente congénita o de aparición en las primeras semanas de vida, con etiología aún desconocida y buen pronóstico, ya que tiene una resolución espontánea en la adolescencia. Presentamos el caso de un paciente quien desde su nacimiento, presentaba una placa en antebrazo derecho, con signo de Darier negativo y asintomatomática. Con los datos clínicos y los antecedentes personales se realiza biopsia de piel, mediante la que confirmamos el diagnóstico de mastocitoma solitario.
Solitary mastocytoma is the second most frequent disease within mastocytosis. It is characterized by a hyperplasia of the mastocitos tissue that affects only the skin. It is usually congenital though it can also appear in the first weeks of life, with unknown etiology; it has a good prognosis due to its spontaneous resolution in the adolescence. This paper presents case of a patient who, from birth, has had some plaque in his right forearm, with negative and asymptomatic Darier's sign. The skin biopsy has been performed with clinical data and personal history, thus confirming the diagnosis of solitary mastocytoma.
ABSTRACT
El objetivo de esta publicación es mostrar un caso de mastocitoma solitario en la vejez, debido a la rareza de su aparición en tal etapa. Sus diagnósticos diferenciales y la involución total de la lesión con el uso de apósitos hidrocoloides, son comentados.
We present a case of a solitary mastocytoma in a man 86 years old who developped the lesion on the inferior lip. The interest of the case is the rarity of the presentation in an adult, which presents others differential diagnostics, and the success of the treatment with hidrocolloid dressings.
Subject(s)
Humans , Male , Aged, 80 and over , Mastocytoma, Skin/diagnosis , Mastocytoma, Skin/pathology , Diagnosis, Differential , Mastocytoma, Skin/drug therapyABSTRACT
Congenital smooth muscle hamartomas (CSMHs) usually appear at birth as skin-colored or slightly hyperpigmented patches or plaques on the trunk or extremities and are often covered by and increased amount of vellus hair. Histopathologically, it represents a proliferation of smooth muscle bundles within the dermis(1,2). We herein report on three cases of localized CSMHs; Case 1 was a 2-month-old boy who presented with a skin-colored, 6x5cm-sized plaque with folds, hypertrichosis and pseudo- Darier's sign on the face, an unusual site. But there was no hyperpigmentation. Case 2 and 3 were both 1-month-old boys who presented with typical hyperpigmented, hairy plaques on the lateral aspect of the left thigh.
Subject(s)
Humans , Infant , Infant, Newborn , Male , Extremities , Hair , Hamartoma , Hyperpigmentation , Hypertrichosis , Muscle, Smooth , Parturition , ThighABSTRACT
Congenital smooth muscle hamartoma usually presents as a well-circumscribed, hypertrichotic, hyperpigmented or skin colored patch or plaque on the trunk or an extremity at birth. Histologically, numerous thick, long, well defined bundles of smooth muscle fibers are scattered throughout the dermis in various directions. We report a case of congenital smooth muscle hamartoma in an 8-month-old female infant who showed hypertrichotic, skin colored plaque on the lumbosacral area since at birth. The pseudo-Darier sign was positive. Histopathologic findings were numerous, well-defined bundles of smooth muscle fibers in the dermis (H and E, Masson-trichrome stain).