ABSTRACT
e extra-adrenal pheochromocytoma.
ABSTRACT
Pheochromocytoma are known to develop at extraadrenal locations in about 10%, however primary cardiac pheochromacytoma account for fewer than 50 cases in the medical literature. We experienced a case of intrapericardial mass in a 60 years old male patient with typical presentation of pheochromocytoma. A functioning extra adrenal pheochromocytoma was diagnosed by means of a biochemical study and radiologic imaging study. We successfully removed a 6.5 x 4.5 x 2.5 cm sized mass between the main pulmonary artery and ascending aorta within the pericardial space. We report the first case of an intrapericardial pheochromocytoma in Korea with a review of literature.
Subject(s)
Humans , Male , Middle Aged , Aorta , Korea , Paraganglioma , Pheochromocytoma , Pulmonary ArteryABSTRACT
TWe report a 18-year-old man, who has been taking antihypertensive medication for 1month in a local clinic, presented with a sudden onset headache followed by left blindness. He experienced palpitation and chest discomfort during physical exertion since 2years before admission, but unfortunately has been ignored. Brain CT showed intracerebral hemorrhage in the left temporoparietal area, but cerebral angiogram and magnetic resonance image revealed no vascular anomaly. He was managed conservatively, and headache and visual loss were improved over time. Subsequently, on the evaluation of hypertension, he was diagnosed as having extra-adrenal pheochromocytoma on left paraaortic area from the results of endocrinological evaluations, abdominal CT scan, and 131I-MIBG scintigraphy.
Subject(s)
Adolescent , Humans , Blindness , Brain , Cerebral Hemorrhage , Headache , Hematoma , Hypertension , Pheochromocytoma , Physical Exertion , Radionuclide Imaging , Thorax , Tomography, X-Ray ComputedABSTRACT
Pheochromocytoma is one of the surgically curable hypertensive diseases and can arise wherever chromaffin cells are located. Herein, a case of extra-adrenal pheochromocytoma developed in a 51 year-old male is presented with brief review of literatures.
Subject(s)
Humans , Male , Middle Aged , Chromaffin Cells , PheochromocytomaABSTRACT
Pheochromocytomas can arise wherever chromaffin cells are found, and most of them(90%) are in one or both adrenal glands. But they may be located anywhere along the sympathetic chain and rarely in aberrant sites. One of the common extra-adrenal sites from which these tumors can arise is a collection of para-aortic and para-ganglion cells around the origin of the inferior mesenteric artery. We experienced a case of extra-adrenal pheochromocytoma located at the organ of Zukerkandl in a 21-year-old female patient with abdominal colic and paroxysmal hypertension, whose symptoms and blood pressure returned to normal after successful surgical excision of the tumor.