ABSTRACT
Dermatofibrosarcoma protuberans (DFSP) is characterized clinically by a locally aggressive growth and a high rate of local recurrence, but distant metastases and tumor related deaths are very rare. Several histologic variants have been described. Among them, sarcomatous change in DFSP represents a form of tumor progression and is associated with a worse prognosis than ordinary DFSP. As a result, it needs more intense treatment and close follow-up care after treatment. A 50-year-old woman presented with a 6 month history of a solitary, walnut-sized, erythematous, hard fixed nodule on her right lower abdomen. Histopathologic examination revealed increased cytologic atypia and mitotic activity with a herringbone growth pattern and negativity for CD34. We report a case of fibrosarcomatous dermatofibrosarcoma protuberans treated by wide surgical excision.