ABSTRACT
El hemangiolinfangioma es un tipo muy raro de malformación del sistema vascular, caracterizado histológicamente por la presencia de vasos venosos y linfáticos dilatados quísticamente, cuyas células endoteliales de revestimiento son positivas para marcadores de inmunohistoquímica como CD31, CD34 y D2-40. El compromiso extenso retroperitoneal y del tracto gastrointestinal es infrecuente. Se presenta el caso de una paciente femenina de 24 años con antecedente de dolor pélvico crónico, con exacerbación de síntomas. El diagnóstico imagenológico mostró una masa retroperitoneal multiquística. Se hizo hemicolectomía derecha y resección de la masa, encontrándose que dicha lesión estaba íntimamente adherida al mesenterio con compromiso extenso del tracto gastrointestinal, y cuyo estudio histopatológico reveló un hemangiolinfangioma, con mejoría clínica posterior a la resección quirúrgica. Aportamos a la literatura mundial, la caracterización de los hallazgos clínicos, imagenológicos e histopatológicos de este tipo de malformaciones
Hemangiolymphangioma is a very rare type of malformation of the vascular system, characterized histologically by the presence of cystically dilated venous and lymphatic vessels, whose lining endothelial cells are positive for immunohistochemical markers such as CD31, CD34 and D2-40. Extensive retroperitoneal and gastrointestinal tract involvement is uncommon. We present the case of a 24-yearold female patient with a history of chronic pelvic pain with exacerbation of symptoms. The imaging diagnosis revealed a multicystic retroperitoneal mass. A right hemicolectomy and resection of the mass was performed, finding that the lesion was intimately adherent to the mesentery with extensive involvement of the gastrointestinal tract, and whose histopathological study revealed a hemangiolymphangioma, with clinical improvement after surgical resection. We contribute to the world literature with the characterization of the clinical, imaging and histopathological findings of this type of malformations
Subject(s)
Humans , Female , Young Adult , Peritoneal Neoplasms/diagnosis , Hemangioma/diagnosis , Lymphangioma/diagnosis , Mesentery/pathology , Peritoneal Neoplasms/surgery , Peritoneal Neoplasms/pathology , Endothelial Cells/pathology , Vascular Malformations/diagnosis , Vascular Malformations/pathology , Hemangioma/surgery , Hemangioma/pathology , Lymphangioma/surgery , Lymphangioma/pathologyABSTRACT
@#This is a case of a fetus with a complex cystic structure on the mid-thorax to the lumbar area detected by ultrasonography at 23 weeks age of gestation. There were no other structural abnormalities noted. The fetal Doppler of the middle cerebral and umbilical arteries were normal. The increase in size of the cystic mass, diagnosed as lymphangioma, and the appearance of pleural effusion at 27 weeks age of gestation prompted further surveillance with magnetic resonance imaging. It showed an extensive subcutaneous mass involving the right thoraco- lumbar region, to consider hemangioma. Expectant management, bringing the pregnancy close to term as possible, was planned. However, the progression of the effusion to the bilateral hemithorax and presence of fetal ascites led to the cesarean delivery of a live preterm male with a birthweight of 1,885 grams (4 lbs 1 oz), maturity index of 29 weeks and an Apgar score of 4, 7, 8 at the first, fifth and tenth minute of life. There was a 15 x 13 cm hemangiolymphangioma on the right thoraco-lumbar area. An ultrasound-guided thoracentesis was done to help alleviate fetal distress. The infant was observed in the neonatal intensive care unit and was sent home stable. Presently, the hemangiolymphangioma is gradually resolving.
Subject(s)
Vascular Malformations , Lymphangioma , HemangiomaABSTRACT
Hemangiolymphangioma is a malformation of both lymphatic and blood vessels. While a hemangiolymphangioma is a benign lesion, its propensity to invade underlying tissues and to recur locally distinguishes it from the simple lymphangioma or hemangioma. Hemangiolymphangiomas are uncommon developmental anomalies and intraosseous hemangiolymphangioma of the mandible is a relatively rare condition: when it occurs, the clinical and radiographic presentation are often nonspecific. The author presents a case of hemangiolymphangioma in mandible.