ABSTRACT
PURPOSE: The oral teratoma is found approximately in live birth at the rate from 1:35,000 to 1:200,000. In a review of literature 16 cases of midline teratoma with cleft palate were reported. We report a case of congenital palatal teratoma with cleft palate in a 1-year-old girl. METHODS: A 1-year-old girl was admitted our institution for the closure of cleft palate. On the intraoperative findings there was 4x1x0.5cm sized hairy soft mass at the midline and complete cleft palate. We did incisional biopsy intraoperatively and its pathology revealed heterotopic brain tissue. The excision of remaining mass and palatoplasty with Sommerlad's method were performed. The final pathology of the mass was mature cystic teratoma. RESULTS: After the operation there were neither recurrence nor oronasal regurgitation. CONCLUSION: We report for one patient with congenital palatal teratoma associated with cleft palate and obtained an excellent result.