ABSTRACT
Ameloblastoma occurs most commonly at the jaw and accounts for 1% of all tumors of jaw. There have been much arguments about ameloblastoma in name, development, classification and treatment. According to the histologic classification of tumors announced by WHO, ameloblastoma had been classified as benign and malignant. And now it is classified as unicystic, multicystic and peripheral ameloblastoma. It has both benign and partially invasive, malignant character. It occurs commonly at the mandible and rarely at the maxilla. According to statistics, it occurs at the mandible 80-95% and at the maxilla 5-20%. We have experienced a case of ameloblastoma occurring in the maxilla, and treated with infrastructure maxillectomy. The histopathologic diagnosis was a acanthomatous ameloblastoma. So, we present this case with a review of literature.