ABSTRACT
La atrofodermia lineal de Moulin es una patología poco frecuente que se presenta en niños sanos y adultos jóvenes. Se manifiesta con lesiones que siguen las líneas de Blaschko. Ocurre sin estar precedida de inflamación, induración, esclerodermia o atrofia epidérmica.Debemos hacer diagnóstico diferencial principalmente con atrofodermia idiopática de Pasini y Pierini y morfea. Tiene pronóstico favorable y no se la ha asociado a otras anomalías. Los tratamientos descritos han sido poco favorables. Presentamos el caso de unamujer de 15 años, con lesiones lineales en dorso y brazo, compatibles con atrofodermia lineal de Moulin.
The linear atrophoderma of Moulin is a rare disease that occurs in healthy children andyoung adults. It manifests with lesions along the lines of Blaschko. It occurs without precedinginflammation, induration, scleroderma or epidermal atrophy. Primarily, we shouldmake the differential diagnosis with idiopathic atrophoderma of Pasini and Pierini andmorphea. It has a favorable prognosis and it has not been associated with other anomalies.The treatments described have been unsuccessfull. We report a 15-year-old woman,with linear lesions on the back and arm compatible with linear atrophoderma of Moulin.
Subject(s)
Humans , Atrophy , Skin Diseases , Dermis/pathology , Skin/pathologyABSTRACT
Linear atrophoderma of Moulin is a disease characterized by hyperpigmented linear atrophoderma which follows Blaschko's lines. There is no preceding inflammation or subsequent sclerodermatous changes. The disease had not been reported in Korean literature since Moulin reported for the first time in 1992. The patient was a 21-year-old Korean female who presented multiple hyperpigmented linear macules on the face, arm and lower extremities since birth. All the lesions followed Blaschko" lines. Histopathologic findings showed mild acanthosis and perivascular lymphohistiocytic infiltration. No changes of dermal collagen and elastic fibers were observed.