Lymphangioma circumscriptum of scrotum: a rare case

Lymphangioma circumscriptum (LC) is a form of lymphatic hamartoma, which mainly involves the skin and subcutaneous tissues. The mucosa of the mouth, tongue, groin, trunk, and axilla are the most common locations of LC, and the scrotum is a rare site of occurrence. Here we report a case of LC of scrotum occurring in a 58-year-old man without any history of surgery and radiation. The man was presented with multiple small vesicles containing clear fluid in the scrotum and subsequent histopathology confirmed the diagnosis. We are presenting this case for its rare presentation.

Acquired Lymphangioma Circumscriptum of Vulva Mimicking Genital Wart: The Utility of Dermoscopy in Differential Diagnosis / 대한피부과학회지

No abstract available.

Vulvar Lymphangioma Circumscriptum.

Lymphangioma circumscriptum (LC) is a rare benign disorder of lymphatic channels in deep dermal and subcutaneous layers. Typically fluid filled vesicles that contain lymphatic fluid with frogspawn-like appearance are seen over any part of body. Vulvar LC is seen as congenital condition or might develop secondary to radiotherapy or surgery. LC involving the vulva is very rare; only 33 cases of vulvar LC have been reported. Surgical treatment is the most commonly used method to treat vulvar LC. In this report we present a case with LC secondary to radiotherapy and lesions regressed with cryotherapy.

Acquired Lymphangioma Circumscriptum of the Vulva Mimicking Condyloma Acuminatum / 대한피부과학회지

Acquired lymphangioma circumscriptum of the vulva is a rare benign disease that arises from obstruction of pelvic lymphatic drainage. It most commonly occurs due to surgery, lymphadenectomy and/or radiotherapy for cervical cancer and it may also result from treatment of other tumor or non-neoplastic diseases such as Crohn's disease or tuberculosis. Epidermal reactive changes due to recurrent infections or stimuli occur in some cases and the vulva lesions can mimic condyloma acuminatum or other viral or fungal infections. Herein we describe a case of acquired lymphangioma circumscriptum of the vulva that mimicked condyloma acuminatum and this all presented 13 years after surgery for cervical cancer in a 71 year old woman.

A Case Report of Lymphangioma Circumscriptum on Scalp

PURPOSE: Lymphangioma circumscriptum is a rare, congenital benign hamartous malformation, caused by the saccular dilatation of lymph channels lines by normal, single cell, lymphatic endothelia that present as local eruptions of persistent, grouped, translucent vesicles. The lymphangioma circumscriptum lesions may occur on axillary fold shoulder, neck proximal limbs and buccal mucosa. We reported a rare case of lymphangioma circumscriptum on the scalp. METHODS: A 15-year-old girl with a 5x3cm sized lymphangioma circumscriptum on scalp was examined. It was defined a boundry by ultrasound. And then, a tissue crescent type expander with 120cc normal saline was inserted on occipital area for a month. After confirmed safety margin of the excised lymphangioma circumscriptum on frozen biopsy and the scalp flap was elevated and covered with empty space. RESULTS: A histopathologic finding revealed that lymphangioma circumscriptum. During 11 months follow up, no relapse was found. CONCLUSION: We described a rare case of lymphangioma circumscriptum on scalp. By using a tissue expander and excision, we achieved no recurrence and aesthetically satisfactory outcome.

Lymphangioma Circumscriptum of the Scalp Resembling Nevus Sebaceus / 대한피부과학회지

Lymphangioma circumscriptum is a rare, congenital benign hamartous malformation caused by the saccular dilatation of lymph channels lined by normal, single-cell, lymphatic endothelia that present as local eruptions of persistent, grouped, translucent vesicles. The predilection sites of lymphangioma circumscriptum are the tongue, axilla, abdomen, buttocks & groin, but scalp lesions are rare. We report a case of lymphangioma circumscriptum on the scalp of a 12 year old girl, which resembled a nevus sebaceous. She had a solitary, asymptomatic, 4.5 x 4.5 cm sized, normal skin-colored to yellowish grouped vesicular plaque on the scalp.

Lymphangioma Circumscriptum Showing the Clinical Features Resembling Condyloma Accuminatum / 대한피부과학회지

Lymphangioma circumscriptum is an uncommon benign hamartomatous malformation that consists of dilated lymphatic channels lined by normal, single-cell lymphatic endothelia. The diagnosis of lymphangioma circumscriptum is usually made on the basis of clinical characteristics. However, a biopsy is required to exclude other clinically resembling diseases, especially when the lesion shows unusual clinical features. We report a case of recurred perianal lymphangioma circumscriptum in a 13-year-old boy, which showed a verrucous mass having features of condyloma accuminatum.

A Case of Klippel-Trenaunay Syndrome with Lymphangioma Circumscriptum / 대한피부과학회지

Klippel-Trenaunay Syndrome(KTS) is a rare clinical syndrome of children and young adults characterized by port-wine stain, varicose veins and venous malformations, and hypertrophy of soft tissue and bone of the extremity which are involved usually unilateral but occasionally bilateral. Additional variants and complicating features include varicose pulmonary veins, cutaneous lymphangiomas, hemihypertrophy of the face, hyperhidrosis, hypertrichosis, cellulitis, paresthesias, syndactyly, macrodactyly, spina bifida, and decalcification of involved bone. We report a 14-year-old girl with port-wine stain on her both flank and left thigh associated with hypertrophy of left lower extremity. She also has lymphangioma circumscriptum on left thigh, macrodactyly, and syndactyly . To the best of our knowledge, this is the first reported case of KTS with lymphagioma circumscriptum in Korea.

A Case Of Lymphangioma Circumscriptum: Magnetic Resonance Imaging (MRI) in Diagnostic Evalutaion

A 21-year-old male visited our clinic with an erythematous plaque studded with papulovesicules on the right thigh and calf which had been noticed at 3 months after birth. Moving the limb caused intermittent pain. He was diagnosed with lymphangioma circumscriptum which involved muscle layers after checking the skin biopsy and magnetic resonance imaging (MRI). Partial removal of mass resulted in relieving pain on motion.

Lymphangioma circumscriptum on buccal mucosa: a case report

Lymphangioma circumscriptum is a benign disorder of lymphatic channels. The pathologic findings consist of a collection of deep, sequestered subcutaneous lymphatic cisterns which are encircled by smooth muscle. The lymphatic cisterns are communicating with superficial clusters of vesicles through dilated lymphatic channels. The etiology of this lesion is unclear ; however, lymphatic obstruction has been suggested as a possible cause. It is characterized clinically by grouped vesicles, some of which may be filled with serosanguinous fluid. It is an unpleasant, but benign condition conventionally managed by wide local excision, which provides symptom control and often prevents recurrence. Neither long term complication nor association with squamous cell carcinoma has been previously documented. Some cases were reported following mastectomy and radiation therapy or radiation therapy for squamous cell carcinoma of the cervix. We present a 17-year-old patient with lymphangioma circumscriptum developed on buccal mucosa, which developed 3 months after innervated serratus anterior muscle free flap for functional reconstruction of cheek. We suppose that it was caused not only by lymphatic blockage resulted from wide operation but also by chronic masticating local irritation. In review of literatures, we didn't have found any report of lymphangioma circumscriptum developed on buccal mucosa.

Lymphangioma circumscriptum on buccal mucosa: a case report

Lymphangioma circumscriptum is a benign disorder of lymphatic channels. The pathologic findings consist of a collection of deep, sequestered subcutaneous lymphatic cisterns which are encircled by smooth muscle. The lymphatic cisterns are communicating with superficial clusters of vesicles through dilated lymphatic channels. The etiology of this lesion is unclear ; however, lymphatic obstruction has been suggested as a possible cause. It is characterized clinically by grouped vesicles, some of which may be filled with serosanguinous fluid. It is an unpleasant, but benign condition conventionally managed by wide local excision, which provides symptom control and often prevents recurrence. Neither long term complication nor association with squamous cell carcinoma has been previously documented. Some cases were reported following mastectomy and radiation therapy or radiation therapy for squamous cell carcinoma of the cervix. We present a 17-year-old patient with lymphangioma circumscriptum developed on buccal mucosa, which developed 3 months after innervated serratus anterior muscle free flap for functional reconstruction of cheek. We suppose that it was caused not only by lymphatic blockage resulted from wide operation but also by chronic masticating local irritation. In review of literatures, we didn't have found any report of lymphangioma circumscriptum developed on buccal mucosa.

A case of lymphangioma circumscriptum with cystic hygroma / 대한피부과학회지

Lymphangiomas and cystic hygromas are congenital malformatiors of the lymphatic system. They are composed of lymph-containing endothelium-lined spaces which very in size from channels of capillary dimensions to cysts several centimeters in diameter. Both types of lesions are rarely present, in the same patients. We report herein a case of lymphangioma circumscriptum with cystic hygroma on the tongue and the right side of the neck in a 5 year-old boy. The patient had a grop of deep-seated, small, crystal-line vesicles resembling frogs spawn that contained a viscous liquid with hemorrhage in the tongue and a mobile non-tender cystic swelling in the right side of the neck.

A Case of Penile Lymphangioma Circumcriptum / 대한피부과학회지

We report a case of penile lymphangioma circumscriptum developed in a 22- year-old male soldier. Rice-sized papule on glans penis was noted at birth and progressed to yellow straw-colored, peanut-sized, asymptomatic grouped papulovesicles resembling frog spawn. The predilection sites of lymphangioma circumscriptum are the abdomen, axilla and tongue. Glans penis is a very rare site. Histopathologic findings showed papillornatosis, hyperkeratosis and cystically dilated lymph vessels lined by a single layer of endothelial cells.

Solitary angiokeratoma developed in one area of lymphangioma circumscriptum

We describe a boy who developed a dark brown colored nodule in an area of lymphangioma circumscriptum following repeated local injuries. The nodule showed the clinical and pathologic features of solitary angiokeratoma. It is possible that previous injuries predisposed the lesion to the development of solitary angiokeratoma.

A Case of Lymphangioma Circumscriptum of the Vulva / 대한피부과학회지

We present a case of lymphangioma circumscriptum in a 17 year-old girl according to tihe clinical and histopathological findings. This case is unusual in that lesions developed on the vulva and thigh without preceding lymphedema. Our patient had a plaque of grouped vesicle-like papules resembling frog's apawn on The both labia majora of vulva and several scattered, skin tag like soft papules on the right upper thigh of theree years duration. Histopathologic findings showed variable sized, dilatated lymphatic channels lined by single layer of normal endothelial cells confined to the only upper dermis.