ABSTRACT
Neurofibroma is a benign tumor which rarely occurs in the oral cavity. Generally, oral neurofibroma is part of a neurofibromatosis type-1 like syndrome (Von Recklinghausen's disease) and rarely occurs as a solitary lesion of oral cavity. Up to now, few cases have been reported with the solitary neurofibromas of tongue and submandibular gland. The tumor can also be rarely located centrally in the bone. This research presents a central neurofibroma case in the maxillary bone which has no relationship with the neurofibromatosis. (AU)
O neurofibroma é um tumor benigno que raramente ocorre na cavidade oral. Geralmente, oral neurofibroma é parte de da neurofibromatose tipo 1 (Von Recklinghausen's doença) e raramente ocorre como uma lesão solitária da cavidade oral. Até agora, poucos casos foram relatado com os neurofibromas solitários de língua e glândula submandibular. O tumor também raramente pode estar localizado centralmente no osso. Esta pesquisa apresenta um neurofibroma central caso no osso maxilar que não tem relação com a neurofibromatose (AU)
Subject(s)
Humans , Male , Child, Preschool , Neurofibromatosis 1 , Neurofibromatoses , NeurofibromaABSTRACT
Introdución: el neurofibroma es un tumor de comportamiento benigno que se origina de las células de la vaina nerviosa periférica, puede presentarse en forma solitaria o como lesiones múltiples como parte de la enfermedad de Von Recklingha³sen o neurofibromatosis. Los solitarios son de presentación rara y usualmente no se encuentran asociados a síntomas sistémicos. Objetivo: presentar el caso y la revisión bibliográfica en la literatura nacional y extranjera. Paciente: se presenta el caso de una paciente con un tumor solitario en la vulva tratado de forma quirúrgica en el servicio de Ginecología del Hospital Carlos Manuel de Céspedes y del Castillo de Bayamo, Granma, en octubre del 2011. Resultados: se procedió a retirar la lesión quirúrgicamente mediante cirugía escisional con enucleación del tumor y resección de la piel redundante. Conclusión: el diagnóstico histológico se correspondió con neurofibroma
Introduction: neurofibroma is a benign tumor that originates from cells of peripheral nerve sheath. It may occur as solitary or multiple lesions as part of Von Recklinghausen disease or neurofibromatosis. The solitary lesions are rare and usually they are not associated with systemic symptoms. Objective: case presentation and literature review in national and international literature. Patient: we report the case of a patient with a vulvar solitary tumor, treated surgically at the Department of Gynecology of Carlos Manuel de Céspedes y del Castillo Hospital in Bayamo, Granma, in October 2011. Results: we proceeded to surgically remove the lesion by excisional surgery with enucleation of the tumor and resection of redundant skin. Conclusion: the histological diagnosis was consistent with neurofibroma