ABSTRACT
El síndrome de Villaret se define por la afección de los nervios craneales glosofaríngeo (IX), vago (X), espinal (XI) e hipogloso mayor (XII), en conjunción con el síndrome de Horner homolateral a la lesión. Se produce por compresión de estos nervios y de las fibras vecinas del plexo simpático pericarotídeo en la base del cráneo, en particular, en el espacio retroparotídeo. Si bien es un hecho conocido la invasión del sistema nervioso central en el cáncer de pulmón avanzado, esta particular asociación sintomática es extremadamente infrecuente. Presentamos una paciente con diagnóstico reciente de adenocarcinoma de pulmón que desarrolló, en forma simultánea, este síndrome.
Villaret syndrome is defined by the affection of the glossopharyngeal (IX), vagal (X), accessory (XI) and hypoglossal (XII) cranial nerves associated with ipsilateral Horner syndrome. It is caused by the compression of these nerves and the neighboring sympathetic plexus fibers at the base of the skull, particularly in the retroparotid space. Even though the invasion of the central nervous system in patients with advanced lung cancer is a frequent and well known occurrence, this particular symptomatic association is extremely rare. We are reporting the case of a newly diagnosed lung adenocarcinoma patient who is simultaneously developing this syndrome.
Subject(s)
Humans , Female , Aged , Adenocarcinoma/complications , Horner Syndrome/etiology , Cranial Nerve Diseases/diagnostic imaging , Lung Neoplasms/complications , Adenocarcinoma/diagnostic imaging , Horner Syndrome/diagnostic imaging , Cranial Nerve Diseases/etiology , Adenocarcinoma of Lung , Lung Neoplasms/diagnostic imaging , Neoplasm InvasivenessABSTRACT
El síndrome de Villaret está caracterizado por una serie de alteraciones de la unión craniocervical, con un compromiso específico de los nervios craneales IX, X, XI y XII, así como la cadena simpática cervical. Desde la primera descripción realizada por Maurice Villaret, se han descrito algunos casos, donde la gran mayoría de las lesiones están localizadas en el espacio retrofaringeo o retroparotideo, y usualmente corresponde a tumores, lesiones vasculares o procesos infecciosos. Presentamos el caso de una paciente con un síndrome de Villaret secundario a un paraganglioma cervical.
Villaret's syndrome is a clinical condition characterized by a compromise of the craniocervical junction, with specific involvement of the cranial nerves IX, X, XI and XII as well as the cervical sympathetic chain. Since the first description by Maurice Villaret, some cases have been described, in which the vast majority of the lesions are located in the retropharyngeal or retroparotid space, and usually correspond to tumors, vascular lesions or infectious processes. We present the case of a female patient with Villaret's syndrome secondary to a cervical paraganglioma.
Subject(s)
Paraganglioma , Deglutition Disorders , Adult , NeoplasmsABSTRACT
A partir do relato de um caso sobre a síndrome de Villaret, o autor ressalta a importância da relação anátomo-clínica, aspectos clínicos e etiologias das síndromes que cursam com o comprometimento dos quatro últimos nervos cranianos quando da sua passagem extracranial.
From the case study of a patient with the Villaret syndrome the author emphasizes the importance of the anatomical-clinical relationship, clinical aspects, and etiologies of syndromes that are associated with the impairment of the last four cranial nerves during its out of skull passage.