ABSTRACT
Se presenta el caso de un lactante menor con tumoración cutánea benigna, localizada en el área submandibular izquierda de la cabeza, característico de un mastocitoma solitario. Su reconocimiento clínico precoz y la instauración terapéutica temprana aceleraron el tiempo de resolución, casi siempre espontánea.
We present a case of an infant with benign cutaneous tumor, located in the left submandibular aspect of the head consistent with solitary mastocytoma. Its early clinical recognition and early treatment onset accelerates time to resolution almost always spontaneous.
ABSTRACT
Se presenta el caso de un lactante menor con tumoración cutánea benigna localizada en el aspecto submandibular izquierdo de la cabeza compatible con mastocitoma cutáneo solitario. Esta rara lesión tumoral es parte del grupo heterogéneo de las mastocitosis, conjunto de enfermedades que resulta de la infiltración anómala de mastocitos en diferentes tejidos corporales, afectando particularmente la piel.La variedad más común de mastocitosis en niños es la urticaria pigmentosa, seguida del mastocitoma cutáneo que contabiliza entre el 10 y 15% de todos los casos. Suele situarse en tronco o extremidades, aunque como en este paciente puede localizarse en cabeza uotros sitios corporales. Es de aparición precoz durante la primera infancia o alguna vez congénito; por lo regular no hay participación de órganos internos o situaciones potencialmente letales. Su curso es crónico con remisiones parciales y exacerbaciones sintomáticasmolestas como fenómenos de urticación y desarrollo de ampollas frente a estímulos externos o internos que preocupan a los familiares cercanos. Su reconocimiento clínico precoz y la pronta instauración terapéutica con esteroides locales, antihistamínicos orales u otras medidas pertinentes, aceleran el tiempo de resolución casi siempre espontánea hacia los 2 años de vida; es importante la debida explicación a los padres
This is a report the case of an infant with benign cutaneous tumor located in the left submandibular aspect of the head support solitary cutaneous mastocytoma. This rare tumor lesion is part of the heterogeneous group of mastocytosis, group of diseases resulting from abnormal infiltration of mast cells in various body tissues, particularly affecting the skin. The most common variety of mastocytosis inchildren is urticaria pigmentosa, followed by cutaneous mastocytoma counted between 10 and 15% of all cases. Usually located on the trunk or extremities, although as in this patient may be located in the head or other body sites. Is early onset in infancy or congenital ever, usually no involvement of internal organs or life-threatening situations. Its course is chronic symptomatic partial remissions and exacerbations Urtication annoying as phenomena and development of blisters against external or internal stimuli which trouble close relatives. Its early clinical recognition and prompt establishment local steroid therapy, oral antihistamines or other relevant measures speed time to spontaneous resolution usually 2 years of life, is important due explanation to parents.
Subject(s)
Humans , Male , Infant, Newborn , Mastocytoma/pathology , PediatricsABSTRACT
El objetivo de esta publicación es mostrar un caso de mastocitoma solitario en la vejez, debido a la rareza de su aparición en tal etapa. Sus diagnósticos diferenciales y la involución total de la lesión con el uso de apósitos hidrocoloides, son comentados.
We present a case of a solitary mastocytoma in a man 86 years old who developped the lesion on the inferior lip. The interest of the case is the rarity of the presentation in an adult, which presents others differential diagnostics, and the success of the treatment with hidrocolloid dressings.
Subject(s)
Humans , Male , Aged, 80 and over , Mastocytoma, Skin/diagnosis , Mastocytoma, Skin/pathology , Diagnosis, Differential , Mastocytoma, Skin/drug therapyABSTRACT
El mastocitoma solitario es una variedad de mastocitosis cutánea que se da desde el nacimiento o durante los primeros seis meses de edad. Se presenta como una lesión única macular, placa o nódulo eritematoso, amarillento o hiperpigmentado, que a la fricción es pruriginosa y se torna más eritematosa, edematosa o ampollar; pero también puede presentar signos extralesionales. El curso natural del cuadro es de involución espontánea en la mayoría de casos, pero dependiendo de los signos y síntomas asociados, se indica antihistamínicos, corticoides tópicos o intralesionales, e incluso excisión quirúrgica (AU)
Solitary mastocytoma is a variety of cutaneous mastocytosis, which usually appears in newborns or during the first six months of age. It presents as a single macule, plaque or nodule that can be erythematous, yellowish or hyperpigmented; with friction it becomes pruritic, erythematous, oedematous or bullous, but may also have extralesional signs. The natural course in most cases is spontaneous involution. Depending on the manifestations, antihistamines, topical or intralesional corticosteroids and even surgical excision can be indicated (AU)
Subject(s)
Humans , Female , Child, Preschool , Mastocytoma, Skin , FaceABSTRACT
Nine-month-old female infant was seen with a 7-month history of a nodule on the right temporal scalp, which had gradually increased in size. Stroking of the lesion resulted in urtication and blistering and there were no other cutaneous lesions. The histology showed subepidermal bulla formation and a dense infiltration of mast cells in the papillary and reticular dermis. We present an infant with solitary mastocytoma on the scalp, a rare site.
Subject(s)
Female , Humans , Infant , Blister , Dermis , Mast Cells , Mastocytoma , Scalp , StrokeABSTRACT
We report five cases of solitary mastocytoma. All patients were under one year of age and diagnosed as solitary mastocytoma based on clinicopathologic findings. Skin lesions were found on the right forearm, left hand, left leg, left elbow and left shoulder. They resolved themselves spontaneously resolution within 2 or 3 years.