Takayasu's Arteritis with Aortic Insufficiency as Initial Presentation: A Case Report

Takayasu's disease is the first cause of inflammatory aortitis in young subjects. The disease preferentially affects the women. Takayasu's disease could be a mode of non-specific reaction of the aorta to various infectious or dysimmune etiological factors. Aortic insufficiency is present in 7 to 10% of cases. It is usually moderate. Its mechanism is not unambiguous: direct damage to the aortic valves or dilation of the aortic annulus. Coronary damage responsible for angina or even myocardial infarction are also possible. We report the case of a severe aortic insufficiency secondary to takayasu disease complicated by acute coronary syndrome in a 42-year-old woman.

Asymptomatic Acute Dissection of the Abdominal Aorta as a Rare Complication of Takayasu Disease

The present study describes a case of a 24-year-old who had an asymptomatic acute dissection of the abdominal sub-renal aorta along with an inflammatory syndrome suggestive of Takayasu disease. Aortic dissection is a rare complication of Takayasu's disease that has only been reported a few times in the literature. The type of aortic dissection (type III b, according to the classification of De Bakey and Stanford) confirmed by computed tomography scan of the aorta (CT scan) in our patient. The patient underwent conservative medical treatment.

Chronic Periaortitis – Review and Presentations

Chronic periaortitis is a rare inflammatory condition predominantly affecting the abdominal segment of the aorta. This can present as IgG4 related inflammatory disease, idiopathic retroperitoneal fibrosis, perianeurysmal retroperitoneal fibrosis andinflammatory abdominal aortic aneurysm (IAAA). Aortitis can also be a manifestation of a number of rheumatological large vessel vasculitides such as Takayasu arteritis and giant cell arteritis (GCA). We present three interesting cases of chronic periaortitis and a literature review. The first case showsa classic picture ofIgG4 periaortitis. The second case illustrates periaortitis with retroperitoneal fibrosis, ureteric involvement and hydronephrosis, following abdominal aortic aneurysmal stenting. The final case presents as widespread periaortitis due to Takayasu's disease involving the entire aorta including the arch and root of the subclavian artery

Takayasu's arteritis and Crohn's disease: an unusual association

A arterite de Takayasu e a doença de Crohn são doenças inflamatórias com etiologia desconhecida. Raramente ocorrem de modo concomitante em um mesmo indivíduo, havendo menos de 30 casos relatados na literatura. Este trabalho descreve essa associação em uma paciente de 36 anos de idade portadora de doença de Crohn, que apresentou redução dos pulsos no membro superior esquerdo e pressão arterial de 60/40 mmHg. A angiotomografia evidenciou estenose segmentar de artéria subclávia esquerda e espessamento parietal circunferencial da aorta na transição toracoabdominal entre T10 e L1, estabelecendo o diagnóstico de arterite de Takayasu. Ambas as patologias são mediadas imunologicamente e apresentam granulomas e vasculite granulomatosa, o que contribui para reforçar a hipótese de uma origem imunológica comum no seu desenvolvimento. Acreditamos que este seja o primeiro caso relatado na literatura brasileira da presença concomitante destas duas enfermidades.

Takayasu's arteritis and Crohn's disease are chronic inflammatory diseases with unknown etiology. They rarely occur together in the same individual, with less than 30 cases reported in the literature. This case report describes this association in a 36-year-old woman with Crohn's disease and weak pulses in her left arm with blood pressure of 60/40 mmHg. Angiotomography showed segmental stenosis in the left subclavian artery and circumferential thickening of the aortic wall between T10 and L1, establishing the diagnosis of Takayasu's arteritis. Both are organ-specific and immune-mediated diseases and exhibit granulomas and granulomatous vasculitis, which contribute to reinforce the hypothesis of a common immunologic origin. We believe that this is the first case of concomitant presence of these two diseases reported in the Brazilian literature.

Aneurisma do Seio de Valsalva direito causando compressão coronariana extrínseca / Aneurisma del Seno de Valsalva derecho causando compresión coronaria extrínseca / Right Sinus of Valsalva Aneurysm causing extrinsic coronary compression

O Aneurisma do Seio de Valsalva (ASV) é um distúrbio cardíaco raro. É mais frequentemente um defeito congênito, mas pode ser adquirido. A doença de Takayasu é uma causa extremamente rara desse distúrbio. A maioria dos casos de ASV não-roto é assintomática. A compressão da artéria coronária esquerda é uma manifestação não usual da doença, que pode causar angina, infarto do miocárdio ou morte. Esse relato de caso descreve um paciente negro de 19 anos, do sexo masculino, apresentando um ASV direito não-roto causado por doença de Takayasu, manifestado através de síndrome coronariana aguda, tratada cirurgicamente com sucesso.

Sinus of Valsalva aneurysm is a rare cardiac disorder. It is more frequently a congenital, but it may also be an acquired condition. Takayasu's disease is an extremely rare cause of this disorder. Most cases of unruptured sinus of Valsalva aneurysm are asymptomatic. Compression of the left coronary artery is an unusual manifestation of the disease that can cause angina, myocardial infarction or death. This report describes a 19-year-old black male with an unruptured right sinus of Valsalva aneurysm caused by Takayasu's disease and manifested by an acute coronary syndrome, successfully treated by surgery.

Aneurisma del Seno de Valsalva (ASV) es un disturbio cardíaco raro. Con mayor frecuencia se trata de un defecto congénito, pero puede ser adquirido. La enfermedad de Takayasu es una causa extremadamente rara de este disturbio. La mayoría de los casos de ASV no roto es asintomática. La compresión de la arteria coronaria izquierda es una manifestación no usual de la enfermedad, que puede causar angina, infarto de miocardio o muerte. Este informe de caso describe un paciente negro, de 19 años, del sexo masculino, presentando un ASV derecho no roto causado por enfermedad de Takayasu, manifestado a través de síndrome coronario agudo, tratado quirúrgicamente con éxito.

Perioperative Anesthetic Management of Acute Heart Failure in a Patient with Takayasu's Arteritis Accompanied by Renovascular Hypertension / 대한마취과학회지

Takayasu's disease is a chronic inflammatory arteriopathy of unknown origin, mainly involving the aorta and its larger branches, but often affecting pulmonary circulation as well. It is most prevalent in young women. Common manifestations include absent pulses, bruits, hypertension (due to renal arterial involvement), left heart failure, stroke, syncope, ocular symptoms, and claudication of the limbs. We present the case of a 44 year old woman who underwent aortoiliac bypass surgery under diagnosis of renovascular hypertension, but showed acute heart failure and died in ICU after surgery. We could postulate the development of right heart failure in this patient based upon the persistant increase of central venous pressure after cross clamping of the abdominal aorta.

Anesthetic Experience of Takayasu Arteritis Following Operation - A case report / 대한마취과학회지

Takayasu Arteritis is a systemic disease of unknown cause characterized by occlusion of the thoracic and aMominal aorta and its branches. Although it is typically a disease of young oriental women, the disease is occasionally reported in other groups. A 29-year-old pregnant woman was admitted for emergency cesarean section. Anethesia was induced with thiopental and succinylcholine and maintained with vecuronium-nitrous oxide-oxygen. After delivery, anesthesia was supplemented with fentanyl and droperidol. After delivery we couldnt detect radial arterial blood pressure in both side. Our experience would provide basic information regarding possible emergency surgery for patients with this intractable disease.

Anesthetic Experience of Takayasu Arteritis Following Operation - A case report / 대한마취과학회지

Takayasu Arteritis is a systemic disease of unknown cause characterized by occlusion of the thoracic and aMominal aorta and its branches. Although it is typically a disease of young oriental women, the disease is occasionally reported in other groups. A 29-year-old pregnant woman was admitted for emergency cesarean section. Anethesia was induced with thiopental and succinylcholine and maintained with vecuronium-nitrous oxide-oxygen. After delivery, anesthesia was supplemented with fentanyl and droperidol. After delivery we couldnt detect radial arterial blood pressure in both side. Our experience would provide basic information regarding possible emergency surgery for patients with this intractable disease.

A Case of Takayasu's Disease

Takayasu's disease is characterized by absent upper extremity pulses and ophthalmological finding of secreased visions and catract formation. Clinical features of Takayasu's disease are attributed to an obstructive arteritis of the large vessels criginating from aortic arch and other aortic segments. This dissease most frequently has been reported from Orient, and has affected primarily young females. This is a report of a 10 years old girl who developed the typical clinical and pathophysiological manifestation of Takayasu's disease and we also made brief review of literature.