ABSTRACT
El síndrome de Swyer-James-MacLeod (SSJM) ocurre como el resultado de una bronquio-litis obliterante en la niñez. Generalmente, este desorden es diagnosticado en niños, después de evaluar infecciones respiratorias recurrentes. Una de las razones para explicar la dificultad en el diagnóstico es que cuando los pacientes desarrollan pequeñas bronquiecta-sias y pocos síntomas no es fácil reconocer sino hasta la edad adulta. Existen pocas referencias de la enfermedad en niños, por lo que consideramos de interés su descripción. Se presenta el caso de un paciente de 4 años con síntomas respiratorios de neumonía aguda y se señalan los aspectos diagnósticos de mayor relevancia clínica actual.
Swyer-James-MacLeod Syndrome (SJMS) occurs as a result of childhood bronchiolitis obliterans. Typically, this disorder is diagnosed in childhood after evaluations for recu-rrent respiratory infections. One of the reasons to explain the difficulty in diagnosis is that when patients develop little bronchiectasis, and therefore, few symptoms, then this syndrome may not be recognized until adulthood. There are few references of the disease in children sowe think your description is interes-ting, we present the case of a 4 year old patient with acute respiratory symptoms of pneumonia, high lighting the most important aspects of clinical diagnosis today.
ABSTRACT
The Swyer-James Syndrome is a acquired pulmonary disease following bronchiolitis obliterans in young aged children, in which characteristic unilateral hyperlucence radiologically. Since Swyer and James first reported a case in 1953, it also has been named unilateral hyperlucent lung syndrome or MacLeod syndrome. Frequently there are repeated pulmonary infections which cause bacterial pneumonia and brochiectasis. In cases of pulmonary symptoms, it is diagnosed at early childhood, but there will be delayed detection until later ages in asymptomatic ones unless occasional chest radiography. Altogether the syndrome begins at childhood and manifested decreased exercise tolerance and failure to thrive, which means important disorder in pediatrics. Presently we experienced Swyer-James syndrome of 4 years old boy who had productive cough for 1 month diagnosed with a plain chest X-ray, lung computerized tomography and isotope lung scanning.
Subject(s)
Child , Child, Preschool , Humans , Male , Bronchiolitis Obliterans , Cough , Exercise Tolerance , Failure to Thrive , Lung , Lung Diseases , Lung, Hyperlucent , Pediatrics , Pneumonia, Bacterial , Radiography , ThoraxABSTRACT
A 32-year-old woman was admitted to the hospital complaining of cough, sputum, and chest discomfort for the past ten days. The radiologic findings were transradiant left lung with reduced number and size of vessels, mediastinal shifting to the right at expiration, matched entilation-perfusion defect on ventilation-perfusion scan, and diffuse hypoplasia of the left pulmonary artery and its branches on pulmonary angiography. We describe a case of unilateral hyperlucent lung by main bronchus obstruction in a patient who presents with a clinical picture suggestive of Swyer-James syndrome.
Subject(s)
Adult , Female , Humans , Angiography , Bronchi , Cough , Lung , Lung, Hyperlucent , Pulmonary Artery , Sputum , ThoraxABSTRACT
The Swyer-James syndrome is a relatively uncommon disease entity presented with unilateral hyperlucent lung due to hypoplasia of a pulmonary artery and bronchiectasis of the affected lung. The main finding is a hyperlucent lung with small hilar shadows on the chest X-ray. Pulmonary angiography is the standard method for diagnosis. We report a case of the Swyer-James syndrome with a brief review of literature.